GenTIGSA Gene Database on Rare Genetic Disorders

Lists of Rare Genetic Disorders  

Vitelliform Macular Dystrophy 2(Best disease)      Explore Disorder's Alias
An Autosomal dominant mode(s) within the Eye disorders category
Reported Pathogenic variants
Candidate Gene Information
S.No. Name/GeneID Description Cytogentic Band Gene Location on genomic DNA Gene Length Exons Details Gene Cross-References
1 BEST1/7439 bestrophin 1 11q12.3 Chr11, NC_000011.10
(61949821..61965515)
15695 nt 13 More... OMIM gene
gnomAD browser
EnsEMBL
GeneCards
ClinGen gene

2 IMPG2/50939 interphotoreceptor matrix proteoglycan 2 3q12.3 Chr3, NC_000003.12
(101222546..101320575, complement)
98030 nt 19 More... OMIM gene
gnomAD browser
EnsEMBL
GeneCards
ClinGen gene

3 IMPG1/3617 interphotoreceptor matrix proteoglycan 1 6q14.1 Chr6, NC_000006.12
(75921114..76072662, complement)
151549 nt 17 More... OMIM gene
gnomAD browser
EnsEMBL
GeneCards
ClinGen gene

Variant Information       
Disorder Cross-References:      Orphanet          OMIM          GARD          GTR          MedGen          MalaCards          EMBL-EBI OLS    Monarch Initiative          NORD     

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