GenTIGSA Gene Database on Rare Genetic Disorders

Bestrophin 1 (BEST1) Associated conditions:  1. Retinitis pigmentosa  2. Stargardt disease 
mRNA Information: Transcript Variants and Protein Isoforms
SNo. Status mRNA accession Protein accession Genomic DNA accession (Chromosome) mRNA location on genomic DNA Assembly UniProtkb ID
1 REVIEWED NM_001139443.3 NP_001132915.1 NC_000011.10 (61949820..61965514) Reference GRCh38.p14 Primary Assembly -
2 REVIEWED NM_001300786.2 NP_001287715.1 NC_000011.10 (61949820..61965514) Reference GRCh38.p14 Primary Assembly -
3 REVIEWED NM_001300787.2 NP_001287716.1 NC_000011.10 (61949820..61965514) Reference GRCh38.p14 Primary Assembly -
4 REVIEWED NM_001363591.3 NP_001350520.1 NC_000011.10 (61949820..61965514) Reference GRCh38.p14 Primary Assembly -
5 REVIEWED NM_001363592.2 NP_001350521.1 NC_000011.10 (61949820..61965514) Reference GRCh38.p14 Primary Assembly -
6 REVIEWED NM_001363593.3 NP_001350522.1 NC_000011.10 (61949820..61965514) Reference GRCh38.p14 Primary Assembly -
7 REVIEWED NM_001440571.1 NP_001427500.1 NC_000011.10 (61949820..61965514) Reference GRCh38.p14 Primary Assembly -
8 REVIEWED NM_001440572.1 NP_001427501.1 NC_000011.10 (61949820..61965514) Reference GRCh38.p14 Primary Assembly -
9 REVIEWED NM_001440573.1 NP_001427502.1 NC_000011.10 (61949820..61965514) Reference GRCh38.p14 Primary Assembly -
10 REVIEWED NM_001440574.1 NP_001427503.1 NC_000011.10 (61949820..61965514) Reference GRCh38.p14 Primary Assembly -
11 REVIEWED NM_001440575.1 NP_001427504.1 NC_000011.10 (61949820..61965514) Reference GRCh38.p14 Primary Assembly -
12 REVIEWED NM_001440576.1 NP_001427505.1 NC_000011.10 (61949820..61965514) Reference GRCh38.p14 Primary Assembly -
13 REVIEWED NM_004183.4 NP_004174.1 NC_000011.10 (61949820..61965514) Reference GRCh38.p14 Primary Assembly -
14 REVIEWED NR_134580.2 - NC_000011.10 (61949820..61965514) Reference GRCh38.p14 Primary Assembly -

Transcript variants arise from alternative splicing during gene expression, producing multiple mRNA transcripts from a single gene, each encoding distinct protein isoforms.

PubMed Links for Transcript Variants (Isoforms)
Link 1196 reference articles

Variant Information Bestrophin 1 (BEST1Mutation Visualization Dashboard: Pathogenic variant distribution chart

 

IndiGenomes variants: Exploring and mapping pathogenic variants in gene Bestrophin 1 (BEST1)
ClinVar variants:Revealing mutagenic patterns

GO Term of Bestrophin 1 (BEST1)
SNo. Reported in speceis Evidence Qualifier GO term Category Pubmed Link
1Homo sapiensIDAenablesintracellularly calcium-gated chloride channel activityFunction11904445 12907679 18400985 
26720466 35789156 
2Homo sapiensIMPenablesintracellularly calcium-gated chloride channel activityFunction18179881 19853238 21330666 
26200502 
3Homo sapiensIDAcontributes_tochloride channel activityFunction17003041 
4Homo sapiensIDAenableschloride channel activityFunction17003041 
5Homo sapiensIEAenableschloride channel activityFunction
6Homo sapiensTASenableschloride channel activityFunction
7Homo sapiensIPIenablesprotein bindingFunction32296183 
8Homo sapiensTASlocated_incytosolComponent17003041 
9Homo sapiensIBAis_active_inplasma membraneComponent
10Homo sapiensIDAlocated_inplasma membraneComponent26200502 
11Homo sapiensIEAlocated_inplasma membraneComponent
12Homo sapiensTASlocated_inplasma membraneComponent
13Homo sapiensIEAinvolved_inmonoatomic ion transportProcess
14Homo sapiensIDAacts_upstream_of_or_withinchloride transportProcess17003041 
15Homo sapiensIEAinvolved_inchloride transportProcess
16Homo sapiensIEAinvolved_invisual perceptionProcess
17Homo sapiensTASinvolved_invisual perceptionProcess9662395 
18Homo sapiensIDAlocated_inbasal plasma membraneComponent31791063 
19Homo sapiensIEAinvolved_inglutamate secretionProcess
20Homo sapiensISSinvolved_inglutamate secretionProcess
21Homo sapiensTASenablesbicarbonate transmembrane transporter activityFunction
22Homo sapiensIEAenableschannel activityFunction
23Homo sapiensIEAinvolved_inbicarbonate transportProcess
24Homo sapiensTASlocated_inmembraneComponent10737974 
25Homo sapiensIDAlocated_inbasolateral plasma membraneComponent11050159 19853238 21330666 
26200502 
26Homo sapiensIEAlocated_inbasolateral plasma membraneComponent
27Homo sapiensIEAenablesligand-gated channel activityFunction
28Homo sapiensISSenablesligand-gated channel activityFunction
29Homo sapiensIDAinvolved_intransepithelial chloride transportProcess17003041 
30Homo sapiensIEAinvolved_inmonoatomic ion transmembrane transportProcess
31Homo sapiensTASinvolved_inmonoatomic ion transmembrane transportProcess
32Homo sapiensIDApart_ofchloride channel complexComponent17003041 
33Homo sapiensIEApart_ofchloride channel complexComponent
34Homo sapiensIPIenablesidentical protein bindingFunction19372599 
35Homo sapiensIEAinvolved_inregulation of synaptic plasticityProcess
36Homo sapiensISSinvolved_inregulation of synaptic plasticityProcess
37Homo sapiensIDAinvolved_inprotein complex oligomerizationProcess26200502 
38Homo sapiensIEAinvolved_ingamma-aminobutyric acid secretion, neurotransmissionProcess
39Homo sapiensISSinvolved_ingamma-aminobutyric acid secretion, neurotransmissionProcess
40Homo sapiensIEAlocated_inpresynapseComponent
41Homo sapiensIEAlocated_inmembrane microdomainComponent
42Homo sapiensISSlocated_inmembrane microdomainComponent
43Homo sapiensIDAenablesbicarbonate channel activityFunction18400985 
44Homo sapiensIBAinvolved_inchloride transmembrane transportProcess