GenTIGSA Gene Database on Rare Genetic Disorders
  Beta Version

Variants from 536 rare genetic disorders, with a total of 897 reported, submitted from India

Schwartz-Jampel syndrome

An  Autosomal recessive  mode(s) within the Bone disorders  category

Likely pathogenic 3
Uncertain significance 1

Variant name Variant type GRCH38 location Germline classification Molecular consequence dbSNP_ID Submitter
NM_005529.7(HSPG2):c.4220A>G (p.Lys1407Arg) Single nucleotide variant Chr1:21872187 Uncertain significance Missense variant rs2550748902 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_005529.7(HSPG2):c.5296G>A (p.Ala1766Thr) Single nucleotide variant Chr1:21857383 Likely pathogenic Missense variant rs1239294172 .Division of Medical Genetics, Department of Pediatrics, All India Institute of Medical Sciences, New Delhi
NM_005529.7(HSPG2):c.11730C>A (p.Cys3910Ter) Single nucleotide variant Chr1:21830033 Likely pathogenic Nonsense rs1215934207 .Pediatrics Genetics, Post Graduate Institute of Medical Education and Research
NM_005529.7(HSPG2):c.4740+5G>A Single nucleotide variant Chr1:21864095 Likely pathogenic Intron variant rs886039909 .Diagnostics Division, CENTRE FOR DNA FINGERPRINTING AND DIAGNOSTICS

Graph displaying all Indian institutes, the rare genetic disorders they studied, and the variants submitted to ClinVar