GenTIGSA Gene Database on Rare Genetic Disorders

Variants in ClinVar from 539 of 916 Rare Genetic Disorders of GenTIGS

Pseudoachondroplastic spondyloepiphyseal dysplasia syndrome

An  Autosomal dominant  mode(s) within the Bone disorders  category

Conflicting classifications of pathogenicity 2
Likely pathogenic 5
Pathogenic 1
Pathogenic/Likely pathogenic 2

Variant name Variant type GRCH38 location Germline classification Molecular consequence dbSNP_ID Submitter
NM_000095.3(COMP):c.950A>G (p.Asp317Gly) Single nucleotide variant Chr19:18788237 Conflicting classifications of pathogenicity Missense variant rs1601057057 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_000095.3(COMP):c.868G>T (p.Asp290Tyr) Single nucleotide variant Chr19:18788319 Pathogenic Missense variant rs2145903266 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_000095.3(COMP):c.1394G>T (p.Gly465Val) Single nucleotide variant Chr19:18786060 Likely pathogenic Missense variant rs2145900849 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_000095.3(COMP):c.983G>T (p.Cys328Phe) Single nucleotide variant Chr19:18787643 Likely pathogenic Missense variant rs2145902336 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_000095.3(COMP):c.925G>A (p.Gly309Arg) Single nucleotide variant Chr19:18788262 Pathogenic/Likely pathogenic Missense variant rs2145903203 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_000095.3(COMP):c.1416_1421del (p.Asn474_Asp475del) Deletion Chr19:18786033 - 18786038 Likely pathogenic Inframe_deletion rs2055164523 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_000095.3(COMP):c.874T>C (p.Cys292Arg) Single nucleotide variant Chr19:18788313 Pathogenic/Likely pathogenic Missense variant rs2055184939 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_000095.3(COMP):c.1201G>C (p.Asp401His) Single nucleotide variant Chr19:18786585 Likely pathogenic Missense variant rs2055169002 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_000095.3(COMP):c.1309G>A (p.Asp437Asn) Single nucleotide variant Chr19:18786145 Conflicting classifications of pathogenicity Missense variant rs2055165476 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_000095.3(COMP):c.1445A>T (p.Asp482Val) Single nucleotide variant Chr19:18786009 Likely pathogenic Missense variant rs2055164276 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India

Indian Institutes & Variant Submission Overview
Chromosome-wise Variant Distribution