GenTIGSA Gene Database on Rare Genetic Disorders

Variants in ClinVar from 539 of 916 Rare Genetic Disorders of GenTIGS

Pfeiffer syndrome

An  Autosomal dominant  mode(s) within the Bone disorders  category

Conflicting classifications of pathogenicity 1
Pathogenic 3

Variant name Variant type GRCH38 location Germline classification Molecular consequence dbSNP_ID Submitter
NM_023110.3(FGFR1):c.66G>C (p.Arg22Ser) Single nucleotide variant Chr8:38457381 Conflicting classifications of pathogenicity Missense variant|5 prime UTR variant rs17175750 .Laboratory of Cyto-molecular Genetics, Department of Anatomy, All India Institute of Medical Sciences (AIIMS), New Delhi
NM_023110.3(FGFR1):c.755C>G (p.Pro252Arg) Single nucleotide variant Chr8:38424690 Pathogenic Missense variant rs121909627 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_000141.5(FGFR2):c.833G>T (p.Cys278Phe) Single nucleotide variant Chr10:121520085 Pathogenic Missense variant|non-coding transcript variant|intron variant rs776587763 .Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics
.Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_000141.5(FGFR2):c.1024T>C (p.Cys342Arg) Single nucleotide variant Chr10:121517379 Pathogenic Missense variant|non-coding transcript variant|intron variant rs121918488 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India

Indian Institutes & Variant Submission Overview
Chromosome-wise Variant Distribution