GenTIGSA Gene Database on Rare Genetic Disorders

Variants in ClinVar from 539 of 916 Rare Genetic Disorders of GenTIGS

Osteogenesis imperfecta

An  Autosomal dominant, Autosomal recessive, X-linked dominant  mode(s) within the Bone disorders  category

Benign/Likely benign 1
Conflicting classifications of pathogenicity 4
Likely pathogenic 15
Pathogenic 18
Pathogenic/Likely pathogenic 10
Uncertain significance 10

Variant name Variant type GRCH38 location Germline classification Molecular consequence dbSNP_ID Submitter
NM_006129.5(BMP1):c.1215C>G (p.Ile405Met) Single nucleotide variant Chr8:22194092 Uncertain significance Missense variant|non-coding transcript variant rs1586459952 .Paediatric Orthopaedics Research Lab, Christian Medical College
NM_006129.5(BMP1):c.916A>C (p.Ser306Arg) Single nucleotide variant Chr8:22179784 Uncertain significance Missense variant|non-coding transcript variant rs1357950133 .Paediatric Orthopaedics Research Lab, Christian Medical College
NM_001854.4(COL11A1):c.3619G>A (p.Gly1207Ser) Single nucleotide variant Chr1:102923371 Uncertain significance Missense variant|non-coding transcript variant rs1234981157 .Paediatric Orthopaedics Research Lab, Christian Medical College
NM_000088.4(COL1A1):c.1663C>A (p.Pro555Thr) Single nucleotide variant Chr17:50194135 Likely pathogenic Missense variant .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_000088.4(COL1A1):c.4342G>C (p.Gly1448Arg) Single nucleotide variant Chr17:50185555 Likely pathogenic Missense variant rs2509152842 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_000088.4(COL1A1):c.3653C>T (p.Ala1218Val) Single nucleotide variant Chr17:50186801 Pathogenic/Likely pathogenic Missense variant rs201398339 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_000088.4(COL1A1):c.2831delG Deletion Chr17:50189274 Pathogenic Splice acceptor variant rs2144549369 .Institute of Medical Genetics and Genomics, Sir Ganga Ram Hospital
NM_000088.4(COL1A1):c.2579G>A (p.Gly860Glu) Single nucleotide variant Chr17:50189893 Likely pathogenic Missense variant rs72653142 .Institute of Medical Genetics and Genomics, Sir Ganga Ram Hospital
NM_000088.4(COL1A1):c.3871T>G (p.Cys1291Gly) Single nucleotide variant Chr17:50186451 Likely pathogenic Missense variant rs2144534929 .Institute of Medical Genetics and Genomics, Sir Ganga Ram Hospital
NM_000088.4(COL1A1):c.4189G>T (p.Glu1397Ter) Single nucleotide variant Chr17:50185837 Pathogenic Nonsense rs902407269 .Institute of Medical Genetics and Genomics, Sir Ganga Ram Hospital
NM_000088.4(COL1A1):c.2056G>A (p.Gly686Ser) Single nucleotide variant Chr17:50191859 Likely pathogenic Missense variant rs1404470949 .Institute of Medical Genetics and Genomics, Sir Ganga Ram Hospital
NM_000088.4(COL1A1):c.4166T>C (p.Leu1389Pro) Single nucleotide variant Chr17:50185860 Likely pathogenic Missense variant rs2144531821 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_000088.4(COL1A1):c.2029-1G>T Single nucleotide variant Chr17:50191887 Pathogenic Splice acceptor variant rs1201602830 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_000088.4(COL1A1):c.3281G>C (p.Gly1094Ala) Single nucleotide variant Chr17:50187964 Likely pathogenic Missense variant rs2144542715 .Institute of Medical Genetics and Genomics, Sir Ganga Ram Hospital
NM_000088.4(COL1A1):c.1155+1G>C Single nucleotide variant Chr17:50195566 Pathogenic/Likely pathogenic Splice donor variant rs72648315 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_000088.4(COL1A1):c.1094G>T (p.Gly365Val) Single nucleotide variant Chr17:50195628 Pathogenic/Likely pathogenic Missense variant rs66494876 .Division of Medical Genetics, Department of Pediatrics, All India Institute of Medical Sciences, New Delhi
NM_000088.4(COL1A1):c.2110G>A (p.Gly704Ser) Single nucleotide variant Chr17:50191805 Pathogenic Missense variant rs67368147 .Institute of Medical Genetics and Genomics, Sir Ganga Ram Hospital
NM_000088.4(COL1A1):c.578dup (p.Gly194fs) Duplication Chr17:50198170 - 50198171 Pathogenic/Likely pathogenic Frameshift variant rs1598300304 .Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics
NM_000088.4(COL1A1):c.3055G>T (p.Gly1019Cys) Single nucleotide variant Chr17:50188786 Pathogenic Missense variant rs1598288342 .Paediatric Orthopaedics Research Lab, Christian Medical College
NM_000088.4(COL1A1):c.2172del (p.Gly725fs) Deletion Chr17:50191446 Pathogenic Frameshift variant rs1567757138 .Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics
NM_000088.4(COL1A1):c.769G>A (p.Gly257Arg) Single nucleotide variant Chr17:50197045 Pathogenic Missense variant rs72645321 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_000088.4(COL1A1):c.3141TCCTGGTGC[1] (p.1047APG[2]) Microsatellite Chr17:50188579 - 50188587 Pathogenic Inframe_deletion rs74315111 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_000089.4(COL1A2):c.825_842dup (p.Pro281_Arg282insAlaGlyProAlaGlyPro) Duplication Chr7:94409348 - 94409349 Uncertain significance Inframe_insertion .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_000089.4(COL1A2):c.821G>T (p.Gly274Val) Single nucleotide variant Chr7:94409350 Pathogenic Missense variant rs67675951 .Institute of Medical Genetics and Genomics, Sir Ganga Ram Hospital
NM_000089.4(COL1A2):c.1631G>C (p.Gly544Ala) Single nucleotide variant Chr7:94413913 Likely pathogenic Missense variant rs72658135 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_000089.4(COL1A2):c.2711G>A (p.Gly904Glu) Single nucleotide variant Chr7:94425154 Likely pathogenic Missense variant rs775246283 .Institute of Medical Genetics and Genomics, Sir Ganga Ram Hospital
NM_000089.4(COL1A2):c.279+3A>C Single nucleotide variant Chr7:94401623 Likely pathogenic Intron variant rs762201938 .Institute of Medical Genetics and Genomics, Sir Ganga Ram Hospital
NM_000089.4(COL1A2):c.231del (p.Phe77fs) Deletion Chr7:94401570 Pathogenic Frameshift variant rs2115865220 .Institute of Medical Genetics and Genomics, Sir Ganga Ram Hospital
NM_000089.4(COL1A2):c.1630G>T (p.Gly544Cys) Single nucleotide variant Chr7:94413912 Likely pathogenic Missense variant rs72658134 .Institute of Medical Genetics and Genomics, Sir Ganga Ram Hospital
NM_000089.4(COL1A2):c.875G>A (p.Gly292Asp) Single nucleotide variant Chr7:94409404 Pathogenic/Likely pathogenic Missense variant rs1131692167 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_000089.4(COL1A2):c.757G>C (p.Gly253Arg) Single nucleotide variant Chr7:94408788 Uncertain significance Missense variant rs1584318623 .Paediatric Orthopaedics Research Lab, Christian Medical College
NM_000089.4(COL1A2):c.2026-1_2042dup Duplication Chr7:94419496 - 94419497 Conflicting classifications of pathogenicity Splice acceptor variant rs1584325529 .Paediatric Orthopaedics Research Lab, Christian Medical College
NM_000089.4(COL1A2):c.1613G>A (p.Gly538Asp) Single nucleotide variant Chr7:94413895 Conflicting classifications of pathogenicity Missense variant rs1584322496 .Paediatric Orthopaedics Research Lab, Christian Medical College
NM_000393.5(COL5A2):c.4174C>A (p.Leu1392Ile) Single nucleotide variant Chr2:189035095 Uncertain significance Missense variant rs748999143 .Paediatric Orthopaedics Research Lab, Christian Medical College
NM_006371.5(CRTAP):c.634C>T (p.Arg212Ter) Single nucleotide variant Chr3:33124420 Pathogenic/Likely pathogenic Nonsense rs137853944 .Diagnostics Division, CENTRE FOR DNA FINGERPRINTING AND DIAGNOSTICS
NM_021939.4(FKBP10):c.1256+1G>A Single nucleotide variant Chr17:41820462 Pathogenic/Likely pathogenic Splice donor variant .Department Of Genetics, Lifeline Super Speciality Hospital, Adoor.
NM_021939.4(FKBP10):c.1479_1481delinsTCAG (p.Leu494fs) Indel Chr17:41821733 - 41821735 Likely pathogenic Frameshift variant .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_021939.4(FKBP10):c.1399+51del Deletion Chr17:41821112 Benign/Likely benign Intron variant rs10522999 .Centre for Medical Genetics, Mumbai
NM_021939.4(FKBP10):c.918-2A>G Single nucleotide variant Chr17:41819528 Likely pathogenic Splice acceptor variant rs1597907877 .Paediatric Orthopaedics Research Lab, Christian Medical College
NM_000158.4(GBE1):c.1843G>C (p.Ala615Pro) Single nucleotide variant Chr3:81535286 Likely pathogenic Missense variant rs768485124 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_001025295.3(IFITM5):c.119C>T (p.Ser40Leu) Single nucleotide variant Chr11:299372 Pathogenic Missense variant rs786201032 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_001025295.3(IFITM5):c.-14C>T Single nucleotide variant Chr11:299504 Pathogenic 5 prime UTR variant rs587776916 .Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics
.Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_002615.7(SERPINF1):c.194T>C (p.Leu65Pro) Single nucleotide variant Chr17:1769961 Uncertain significance Missense variant|5 prime UTR variant rs760504051 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
.Suma Genomics
NM_002615.7(SERPINF1):c.250dup (p.Ser84fs) Duplication Chr17:1770016 - 1770017 Pathogenic Frameshift variant|5 prime UTR variant .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_022356.4(P3H1):c.2051_2054del (p.Glu684fs) Microsatellite Chr1:42747273 - 42747276 Pathogenic Frameshift variant rs2124076122 .Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics
NM_022356.4(P3H1):c.1980dup (p.Val661fs) Duplication Chr1:42747346 - 42747347 Pathogenic/Likely pathogenic Frameshift variant rs1570453963 .Paediatric Orthopaedics Research Lab, Christian Medical College
NM_022356.4(P3H1):c.2131dup (p.Leu711fs) Duplication Chr1:42746776 - 42746777 Pathogenic/Likely pathogenic 3 prime UTR variant|frameshift variant rs1570452407 .Paediatric Orthopaedics Research Lab, Christian Medical College
NM_022356.4(P3H1):c.1346-1G>C Single nucleotide variant Chr1:42752665 Pathogenic Splice acceptor variant rs886042897 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
.Neuberg Centre For Genomic Medicine, NCGM
NM_000942.5(PPIB):c.399_401dup (p.Gly134_Pro135insGly) Duplication Chr15:64156851 - 64156852 Uncertain significance Inframe_indel|inframe_insertion|3 prime UTR variant|non-coding transcript variant rs886039912 .Diagnostics Division, CENTRE FOR DNA FINGERPRINTING AND DIAGNOSTICS
NM_002615.7(SERPINF1):c.532C>T (p.Gln178Ter) Single nucleotide variant Chr17:1771964 Pathogenic Nonsense|5 prime UTR variant rs2543482778 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_002615.7(SERPINF1):c.-37C>A Single nucleotide variant Chr17:1762085 Uncertain significance 5 prime UTR variant rs1039127862 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_002615.7(SERPINF1):c.826TTC[1] (p.Phe277del) Microsatellite Chr17:1776569 - 1776571 Conflicting classifications of pathogenicity Inframe_deletion rs773952734 .Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics
.Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_002615.7(SERPINF1):c.77dup (p.Glu27fs) Duplication Chr17:1766981 - 1766982 Pathogenic Frameshift variant|intron variant rs1272920425 .Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics
NM_002615.7(SERPINF1):c.907C>T (p.Arg303Ter) Single nucleotide variant Chr17:1776652 Pathogenic/Likely pathogenic Nonsense rs763291398 .GenePathDx, GenePath diagnostics
NM_001235.5(SERPINH1):c.1214G>A (p.Arg405His) Single nucleotide variant Chr11:75572040 Uncertain significance Missense variant rs781125078 .Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics
NM_005430.4(WNT1):c.506dup (p.Cys170fs) Duplication Chr12:48980564 - 48980565 Pathogenic Frameshift variant rs779969402 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
.Neuberg Centre For Genomic Medicine, NCGM
NM_005430.4(WNT1):c.501G>C (p.Trp167Cys) Single nucleotide variant Chr12:48980566 Conflicting classifications of pathogenicity Missense variant rs1592257435 .Paediatric Orthopaedics Research Lab, Christian Medical College
NM_005430.4(WNT1):c.104+4_104+44del Deletion Chr12:48978757 - 48978797 Likely pathogenic Intron variant rs1555178899 .Department of Paediatric Medicine, Post Graduation Institute of Medical Education and Research

Indian Institutes & Variant Submission Overview
Chromosome-wise Variant Distribution