GenTIGSA Gene Database on Rare Genetic Disorders

Variants in ClinVar from 539 of 916 Rare Genetic Disorders of GenTIGS

Fanconi anemia

An  Autosomal recessive, X-linked dominant  mode(s) within the Bone disorders  category

Conflicting classifications of pathogenicity 7
Likely pathogenic 5
Pathogenic 19
Pathogenic/Likely pathogenic 7
Uncertain significance 15

Variant name Variant type GRCH38 location Germline classification Molecular consequence dbSNP_ID Submitter
NM_001408458.1(BRCA1):c.-61-9703_-61-8238del Deletion Chr17:43124017 - 43125482 Uncertain significance Intron variant .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_000059.4(BRCA2):c.4733T>G (p.Leu1578Ter) Single nucleotide variant Chr13:32339088 Pathogenic/Likely pathogenic Nonsense rs2137509604 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_032043.3(BRIP1):c.633del (p.Gly212fs) Deletion Chr17:61808752 Pathogenic Frameshift variant rs779466229
NM_032043.3(BRIP1):c.1897A>C (p.Ile633Leu) Single nucleotide variant Chr17:61780299 Conflicting classifications of pathogenicity Missense variant rs765314472 .Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics
NM_000135.4(FANCA):c.826+2T>C Single nucleotide variant Chr16:89799603 Conflicting classifications of pathogenicity Splice donor variant rs2143585058 .Dept. of Cytogenetics, ICMR- National Institute of Immunohaematology
NM_000135.4(FANCA):c.3409-2A>C Single nucleotide variant Chr16:89746690 Uncertain significance Splice acceptor variant rs2143107119 .Dept. of Cytogenetics, ICMR- National Institute of Immunohaematology
NM_000135.4(FANCA):c.3239+2T>G Single nucleotide variant Chr16:89749728 Uncertain significance Splice donor variant rs1567603724 .Dept. of Cytogenetics, ICMR- National Institute of Immunohaematology
NC_000016.10:g.89839795C>G Single nucleotide variant Chr16:89839795 Uncertain significance Intron variant rs2041486621 .Dept. of Cytogenetics, ICMR- National Institute of Immunohaematology
NM_000135.4:c.710_894del Deletion Chr: Likely pathogenic .Dept. of Cytogenetics, ICMR- National Institute of Immunohaematology
NM_000135.4:c.1901_3240del Deletion Chr: Likely pathogenic .Dept. of Cytogenetics, ICMR- National Institute of Immunohaematology
NM_000135.4:c.1626_2602del Deletion Chr: Pathogenic .Dept. of Cytogenetics, ICMR- National Institute of Immunohaematology
NM_000135.4:c.2853_*580del Deletion Chr: Pathogenic .Dept. of Cytogenetics, ICMR- National Institute of Immunohaematology
NM_000135.4:c.1471_2853del Deletion Chr: Pathogenic .Dept. of Cytogenetics, ICMR- National Institute of Immunohaematology
NM_000135.4:c.894_2015del Deletion Chr: Pathogenic .Dept. of Cytogenetics, ICMR- National Institute of Immunohaematology
NM_000135.4:c.874_2982del Deletion Chr: Pathogenic .Dept. of Cytogenetics, ICMR- National Institute of Immunohaematology
NM_000135.4:c.1019_*580del Deletion Chr: Pathogenic .Dept. of Cytogenetics, ICMR- National Institute of Immunohaematology
NM_000135.4:c.284_1627del Deletion Chr: Pathogenic .Dept. of Cytogenetics, ICMR- National Institute of Immunohaematology
NM_000135.4(FANCA):c.3788T>C (p.Phe1263Ser) Single nucleotide variant Chr16:89740844 Uncertain significance Missense variant|3 prime UTR variant|non-coding transcript variant rs2062115558 .Dept. of Cytogenetics, ICMR- National Institute of Immunohaematology
NM_000135.4(FANCA):c.3792_3794del (p.Leu1265del) Deletion Chr16:89740838 - 89740840 Uncertain significance Inframe_deletion|3 prime UTR variant|non-coding transcript variant rs2151716800 .Dept. of Cytogenetics, ICMR- National Institute of Immunohaematology
.Neuberg Centre For Genomic Medicine, NCGM
NM_000135.4(FANCA):c.3282C>G (p.Ser1094Arg) Single nucleotide variant Chr16:89748725 Conflicting classifications of pathogenicity Missense variant rs761244757 .Dept. of Cytogenetics, ICMR- National Institute of Immunohaematology
NM_000135.4(FANCA):c.1344T>G (p.Tyr448Ter) Single nucleotide variant Chr16:89791418 Pathogenic Nonsense rs1199670660 .Dept. of Cytogenetics, ICMR- National Institute of Immunohaematology
NM_000135.4(FANCA):c.2656G>T (p.Glu886Ter) Single nucleotide variant Chr16:89765012 Pathogenic Nonsense rs1487360770 .Dept. of Cytogenetics, ICMR- National Institute of Immunohaematology
NM_000135.4(FANCA):c.4185dup (p.Ile1396fs) Duplication Chr16:89738956 - 89738957 Pathogenic Frameshift variant|3 prime UTR variant|non-coding transcript variant rs2062046121 .Dept. of Cytogenetics, ICMR- National Institute of Immunohaematology
NM_000135.4(FANCA):c.4085T>A (p.Leu1362Ter) Single nucleotide variant Chr16:89739215 Conflicting classifications of pathogenicity Nonsense|3 prime UTR variant|non-coding transcript variant rs745688750 .Dept. of Cytogenetics, ICMR- National Institute of Immunohaematology
NM_000135.4(FANCA):c.3239+1dup Duplication Chr16:89749728 - 89749729 Pathogenic Splice donor variant rs766989857 .Dept. of Cytogenetics, ICMR- National Institute of Immunohaematology
.Neuberg Centre For Genomic Medicine, NCGM
NM_000135.4(FANCA):c.964C>T (p.His322Tyr) Single nucleotide variant Chr16:89795948 Conflicting classifications of pathogenicity Missense variant rs772768595 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_000135.4(FANCA):c.3761_3762del (p.Glu1254fs) Microsatellite Chr16:89742803 - 89742804 Pathogenic Frameshift variant rs868273545 .Lifecell International Pvt. Ltd
NM_001018113.3(FANCB):c.2165+2T>G Single nucleotide variant ChrX:14844501 Uncertain significance Splice donor variant rs2147389062 .Dept. of Cytogenetics, ICMR- National Institute of Immunohaematology
NM_000136.3(FANCC):c.70C>T (p.Gln24Ter) Single nucleotide variant Chr9:95249222 Pathogenic/Likely pathogenic Nonsense rs2136101386 .Dept. of Cytogenetics, ICMR- National Institute of Immunohaematology
.Neuberg Centre For Genomic Medicine, NCGM
NM_001018115.3(FANCD2):c.2361T>G (p.Phe787Leu) Single nucleotide variant Chr3:10065955 Uncertain significance Missense variant rs765365413 .Dept. of Cytogenetics, ICMR- National Institute of Immunohaematology
NM_001018115.3(FANCD2):c.473C>G (p.Pro158Arg) Single nucleotide variant Chr3:10036321 Uncertain significance Missense variant rs2124978557 .Dept. of Cytogenetics, ICMR- National Institute of Immunohaematology
NM_001018115.3(FANCD2):c.1413+2T>A Single nucleotide variant Chr3:10048053 Uncertain significance Splice donor variant rs1459222478 .Dept. of Cytogenetics, ICMR- National Institute of Immunohaematology
NM_001018115.3(FANCD2):c.571-3C>G Single nucleotide variant Chr3:10039718 Uncertain significance Intron variant rs191386799 .Dept. of Cytogenetics, ICMR- National Institute of Immunohaematology
NM_001018115.3(FANCD2):c.2976+5G>A Single nucleotide variant Chr3:10078202 Conflicting classifications of pathogenicity Intron variant rs748710535 .Dept. of Cytogenetics, ICMR- National Institute of Immunohaematology
NM_001018115.3(FANCD2):c.206-1G>T Single nucleotide variant Chr3:10034468 Likely pathogenic Splice acceptor variant rs2124974541 .Dept. of Cytogenetics, ICMR- National Institute of Immunohaematology
NM_001018115.3(FANCD2):c.4338T>G (p.Ser1446Arg) Single nucleotide variant Chr3:10101244 Uncertain significance Missense variant|intron variant rs2125105648 .Dept. of Cytogenetics, ICMR- National Institute of Immunohaematology
NM_021922.3(FANCE):c.491T>C (p.Leu164Pro) Single nucleotide variant Chr6:35455989 Uncertain significance Missense variant rs1767316710 .Dept. of Cytogenetics, ICMR- National Institute of Immunohaematology
NM_004629.2(FANCG):c.1761-2A>C Single nucleotide variant Chr9:35074218 Likely pathogenic Splice acceptor variant rs765150956 .Lifecell International Pvt. Ltd
.Neuberg Centre For Genomic Medicine, NCGM
NM_004629.2(FANCG):c.1501C>T (p.Gln501Ter) Single nucleotide variant Chr9:35075062 Pathogenic Nonsense rs2131053086 .Dept. of Cytogenetics, ICMR- National Institute of Immunohaematology
NM_004629.2(FANCG):c.1572G>A (p.Trp524Ter) Single nucleotide variant Chr9:35074991 Pathogenic Nonsense rs1461242610 .Dept. of Cytogenetics, ICMR- National Institute of Immunohaematology
NM_004629.2(FANCG):c.1468G>T (p.Glu490Ter) Single nucleotide variant Chr9:35075291 Pathogenic Nonsense rs2131053417 .Dept. of Cytogenetics, ICMR- National Institute of Immunohaematology
NM_004629.2(FANCG):c.1375C>T (p.Gln459Ter) Single nucleotide variant Chr9:35075523 Likely pathogenic Nonsense rs2131053817 .Dept. of Cytogenetics, ICMR- National Institute of Immunohaematology
NM_004629.2(FANCG):c.1252G>T (p.Glu418Ter) Single nucleotide variant Chr9:35075646 Pathogenic/Likely pathogenic Nonsense rs886063896 .Dept. of Cytogenetics, ICMR- National Institute of Immunohaematology
NM_004629.2(FANCG):c.1385C>A (p.Ala462Asp) Single nucleotide variant Chr9:35075513 Uncertain significance Missense variant rs2131053797 .Dept. of Cytogenetics, ICMR- National Institute of Immunohaematology
NM_004629.2(FANCG):c.346C>T (p.Gln116Ter) Single nucleotide variant Chr9:35078305 Pathogenic Nonsense rs1829123346 .Dept. of Cytogenetics, ICMR- National Institute of Immunohaematology
NM_004629.2(FANCG):c.787C>T (p.Gln263Ter) Single nucleotide variant Chr9:35076861 Pathogenic/Likely pathogenic Nonsense rs149721361 .Dept. of Cytogenetics, ICMR- National Institute of Immunohaematology
.Neuberg Centre For Genomic Medicine, NCGM
NM_001113378.2(FANCI):c.3907G>T (p.Glu1303Ter) Single nucleotide variant Chr15:89315372 Pathogenic/Likely pathogenic Nonsense rs544848412 .Dept. of Cytogenetics, ICMR- National Institute of Immunohaematology
NM_001113378.2(FANCI):c.295del (p.His99fs) Deletion Chr15:89261590 Pathogenic/Likely pathogenic Frameshift variant rs759398314 .Dept. of Cytogenetics, ICMR- National Institute of Immunohaematology
NM_018062.4(FANCL):c.1092G>A (p.Lys364=) Single nucleotide variant Chr2:58160108 Pathogenic Synonymous variant rs577063114 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
.Neuberg Centre For Genomic Medicine, NCGM
NM_001018115.3(FANCD2):c.1222C>T (p.Arg408Ter) Single nucleotide variant Chr3:10046667 Conflicting classifications of pathogenicity Nonsense rs771869385 .Dept. of Cytogenetics, ICMR- National Institute of Immunohaematology
NM_058216.3(RAD51C):c.571+1del Deletion Chr17:58696858 Pathogenic/Likely pathogenic Splice donor variant rs1327086366 .Lifecell International Pvt. Ltd
NM_032444.4(SLX4):c.1163+2T>A Single nucleotide variant Chr16:3600977 Pathogenic Splice donor variant rs773642409
NM_000135.4(FANCA):c.3884T>C (p.Leu1295Ser) Single nucleotide variant Chr16:89740044 Uncertain significance Missense variant|3 prime UTR variant|non-coding transcript variant rs986710868 .Dept. of Cytogenetics, ICMR- National Institute of Immunohaematology

Indian Institutes & Variant Submission Overview
Chromosome-wise Variant Distribution