GenTIGSA Gene Database on Rare Genetic Disorders

Variants in ClinVar from 539 of 916 Rare Genetic Disorders of GenTIGS

Dyskeratosis congenita

An  Autosomal dominant, Autosomal recessive, X-linked dominant  mode(s) within the Skin disorders  category

Conflicting classifications of pathogenicity 8
Likely pathogenic 2
Pathogenic 5
Uncertain significance 3

Variant name Variant type GRCH38 location Germline classification Molecular consequence dbSNP_ID Submitter
NM_001363.5(DKC1):c.204C>G (p.His68Gln) Single nucleotide variant ChrX:154765939 Likely pathogenic Missense variant|non-coding transcript variant rs199422245 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_001363.5(DKC1):c.1156G>A (p.Ala386Thr) Single nucleotide variant ChrX:154774602 Pathogenic Missense variant|non-coding transcript variant rs199422252 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_018648.4(NOP10):c.34G>C (p.Asp12His) Single nucleotide variant Chr15:34343040 Conflicting classifications of pathogenicity Missense variant rs146261631 .Dept. of Cytogenetics, ICMR- National Institute of Immunohaematology
NM_001283009.2(RTEL1):c.396-43T>C Single nucleotide variant Chr20:63662503 Uncertain significance Missense variant|intron variant rs771899332 .Dept. of Cytogenetics, ICMR- National Institute of Immunohaematology
NM_001283009.2(RTEL1):c.2932_2944del (p.Tyr978fs) Deletion Chr20:63693221 - 63693233 Pathogenic Non-coding transcript variant|frameshift variant rs2090805858 .Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics
NM_198253.3(TERT):c.1452A>C (p.Glu484Asp) Single nucleotide variant Chr5:1293434 Pathogenic Missense variant|non-coding transcript variant rs2478409320 .Dept. of Cytogenetics, ICMR- National Institute of Immunohaematology
NM_198253.3(TERT):c.2323C>T (p.Gln775Ter) Single nucleotide variant Chr5:1272244 Pathogenic Nonsense rs2478210028 .Dept. of Cytogenetics, ICMR- National Institute of Immunohaematology
NM_198253.3(TERT):c.2746G>A (p.Gly916Ser) Single nucleotide variant Chr5:1264501 Conflicting classifications of pathogenicity Missense variant|intron variant rs1189683846 .Dept. of Cytogenetics, ICMR- National Institute of Immunohaematology
NM_198253.3(TERT):c.902G>T (p.Arg301Leu) Single nucleotide variant Chr5:1293984 Conflicting classifications of pathogenicity Missense variant|non-coding transcript variant rs1268051204 .Dept. of Cytogenetics, ICMR- National Institute of Immunohaematology
NM_198253.3(TERT):c.1828C>T (p.Arg610Trp) Single nucleotide variant Chr5:1280280 Conflicting classifications of pathogenicity Missense variant|non-coding transcript variant rs747940807 .Dept. of Cytogenetics, ICMR- National Institute of Immunohaematology
NM_198253.3(TERT):c.2368G>A (p.Val790Ile) Single nucleotide variant Chr5:1272199 Conflicting classifications of pathogenicity Missense variant rs371413388 .Dept. of Cytogenetics, ICMR- National Institute of Immunohaematology
NM_198253.3(TERT):c.2936G>A (p.Arg979Gln) Single nucleotide variant Chr5:1260508 Conflicting classifications of pathogenicity Missense variant|non-coding transcript variant rs765566930 .Dept. of Cytogenetics, ICMR- National Institute of Immunohaematology
NM_198253.3(TERT):c.2227C>T (p.Arg743Trp) Single nucleotide variant Chr5:1278700 Conflicting classifications of pathogenicity Missense variant|non-coding transcript variant rs1388515349 .Dept. of Cytogenetics, ICMR- National Institute of Immunohaematology
NM_198253.3(TERT):c.2329G>A (p.Val777Met) Single nucleotide variant Chr5:1272238 Conflicting classifications of pathogenicity Missense variant rs1554040129 .Dept. of Cytogenetics, ICMR- National Institute of Immunohaematology
NM_001099274.3(TINF2):c.865C>G (p.Pro289Ala) Single nucleotide variant Chr14:24240615 Likely pathogenic Missense variant rs1555304055 .Dept. of Cytogenetics, ICMR- National Institute of Immunohaematology
NM_001099274.3(TINF2):c.845G>A (p.Arg282His) Single nucleotide variant Chr14:24240635 Pathogenic Missense variant rs121918544 .Dept. of Cytogenetics, ICMR- National Institute of Immunohaematology
.Lifecell International Pvt. Ltd
NM_001143992.2(WRAP53):c.892C>T (p.Arg298Trp) Single nucleotide variant Chr17:7701726 Uncertain significance Missense variant rs1055897133 .Dept. of Cytogenetics, ICMR- National Institute of Immunohaematology
NM_001143992.2(WRAP53):c.767T>C (p.Ile256Thr) Single nucleotide variant Chr17:7701494 Uncertain significance Missense variant rs548123219 .Dept. of Cytogenetics, ICMR- National Institute of Immunohaematology

Indian Institutes & Variant Submission Overview
Chromosome-wise Variant Distribution