GenTIGSA Gene Database on Rare Genetic Disorders

Variants in ClinVar from 539 of 916 Rare Genetic Disorders of GenTIGS

Duchenne muscular dystrophy

An  X-linked dominant  mode(s) within the Neuromuscular disorders  category

Likely pathogenic 6
Pathogenic 15
Pathogenic/Likely pathogenic 1
Uncertain significance 1

Variant name Variant type GRCH38 location Germline classification Molecular consequence dbSNP_ID Submitter
NM_004006.3(DMD):c.10044del (p.Gly3349fs) Deletion ChrX:31180412 Likely pathogenic Frameshift variant .Institute of Medical Genetics and Genomics, Sir Ganga Ram Hospital
NM_004006.3(DMD):c.1327del (p.Ser443fs) Deletion ChrX:32644136 Likely pathogenic Frameshift variant .Institute of Medical Genetics and Genomics, Sir Ganga Ram Hospital
NM_004006.3(DMD):c.1863T>A (p.Tyr621Ter) Single nucleotide variant ChrX:32565831 Likely pathogenic Nonsense .Institute of Medical Genetics and Genomics, Sir Ganga Ram Hospital
NM_004006.3(DMD):c.7437G>A (p.Trp2479Ter) Single nucleotide variant ChrX:31774065 Pathogenic Nonsense rs2149245072 .Institute of Medical Genetics and Genomics, Sir Ganga Ram Hospital
NM_004006.3(DMD):c.8224C>T (p.Gln2742Ter) Single nucleotide variant ChrX:31507447 Pathogenic Nonsense rs2147177872 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_004006.3(DMD):c.9060del (p.Asn3021fs) Deletion ChrX:31444505 Pathogenic Frameshift variant rs2524517271 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_004006.3(DMD):c.8028-1G>T Single nucleotide variant ChrX:31627863 Pathogenic Splice acceptor variant rs2148423696 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_004006.3(DMD):c.4354C>T (p.Gln1452Ter) Single nucleotide variant ChrX:32389665 Pathogenic Nonsense rs2147613652 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_004006.3(DMD):c.3774C>A (p.Cys1258Ter) Single nucleotide variant ChrX:32448468 Pathogenic Nonsense rs1569562933 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
.Neuberg Centre For Genomic Medicine, NCGM
NM_004006.3(DMD):c.9975-1G>T Single nucleotide variant ChrX:31180482 Pathogenic Splice acceptor variant rs1556040444 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NC_000023.10:g.(31697577_31747779)_(31986532_32235089)del Deletion Chr: Pathogenic .Department of Neurogenetics, Institute for Communicative and Cognitive Neurosciences
NM_004006.3(DMD):c.5653C>T (p.Gln1885Ter) Single nucleotide variant ChrX:32343220 Pathogenic Nonsense rs1295935628 .Lifecell International Pvt. Ltd
NM_004006.3(DMD):c.6615-2A>G Single nucleotide variant ChrX:31932229 Pathogenic Splice acceptor variant rs1557011973 .Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics
NM_004006.3(DMD):c.2530C>T (p.Gln844Ter) Single nucleotide variant ChrX:32491369 Pathogenic Nonsense rs768892830 .Diagnostics Services (NGS), CSIR - Centre For Cellular And Molecular Biology
NM_004006.2:c.94_3786dup Duplication Chr: Likely pathogenic .Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics
NM_004006.3(DMD):c.497G>T (p.Gly166Val) Single nucleotide variant ChrX:32816501 Uncertain significance Missense variant rs1557052538 .GenePathDx, GenePath diagnostics
NM_004006.2(DMD):c.94_264dup Duplication Chr: Likely pathogenic .Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics
NM_004006.3(DMD):c.8459G>A (p.Trp2820Ter) Single nucleotide variant ChrX:31496876 Likely pathogenic Nonsense rs886039785 .Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics
NM_004006.3(DMD):c.5530C>T (p.Arg1844Ter) Single nucleotide variant ChrX:32345999 Pathogenic Nonsense rs1064325 .Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics
.Neuberg Centre For Genomic Medicine, NCGM
NM_004006.3(DMD):c.2381-1G>T Single nucleotide variant ChrX:32491519 Pathogenic/Likely pathogenic Splice acceptor variant rs398123887 .Lifecell International Pvt. Ltd
NM_004006.3(DMD):c.5899C>T (p.Arg1967Ter) Single nucleotide variant ChrX:32342123 Pathogenic Nonsense rs128626249 .Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics
NM_004006.3(DMD):c.724C>T (p.Gln242Ter) Single nucleotide variant ChrX:32699219 Pathogenic Nonsense rs128626238 .Institute of Medical Genetics and Genomics, Sir Ganga Ram Hospital
NM_004006.3(DMD):c.2302C>T (p.Arg768Ter) Single nucleotide variant ChrX:32501833 Pathogenic Nonsense rs201366610 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India

Indian Institutes & Variant Submission Overview
Chromosome-wise Variant Distribution