GenTIGSA Gene Database on Rare Genetic Disorders

Variants in ClinVar from 539 of 916 Rare Genetic Disorders of GenTIGS

Desbuquois dysplasia 1

An  Autosomal recessive  mode(s) within the Bone disorders  category

Likely pathogenic 2
Pathogenic/Likely pathogenic 1
Uncertain significance 2

Variant name Variant type GRCH38 location Germline classification Molecular consequence dbSNP_ID Submitter
NM_001159773.2(CANT1):c.836G>A (p.Gly279Asp) Single nucleotide variant Chr17:78993920 Likely pathogenic Missense variant rs1233347902 .Lifecell International Pvt. Ltd
NM_001159773.2(CANT1):c.1186G>C (p.Glu396Gln) Single nucleotide variant Chr17:78993570 Uncertain significance Missense variant rs1198106363 .Lifecell International Pvt. Ltd
NM_001159773.2(CANT1):c.631+11C>A Single nucleotide variant Chr17:78996981 Uncertain significance Intron variant rs2145839791 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_001159773.2(CANT1):c.902_906dup (p.Ser303fs) Microsatellite Chr17:78993849 - 78993850 Pathogenic/Likely pathogenic Frameshift variant rs587776895 .Institute of Medical Genetics and Genomics, Sir Ganga Ram Hospital
NM_001159773.2(CANT1):c.896C>T (p.Pro299Leu) Single nucleotide variant Chr17:78993860 Likely pathogenic Missense variant rs267606700 .Institute of Medical Genetics and Genomics, Sir Ganga Ram Hospital

Indian Institutes & Variant Submission Overview
Chromosome-wise Variant Distribution