GenTIGSA Gene Database on Rare Genetic Disorders
  Beta Version

Variants from 496 rare genetic disorders, with a total of 857 reported, submitted from India

Cutis laxa

An  Autosomal dominant, Autosomal recessive, X-linked dominant  mode(s) within the Skin disorders  category

Conflicting classifications of pathogenicity 1
Likely pathogenic 2
Pathogenic 4
Pathogenic/Likely pathogenic 1
Uncertain significance 1

Variant name Variant type Germline classification Molecular consequence Grch38 Location dbSNP_ID Submitter
NM_002860.4(ALDH18A1):c.1273C>T (p.Arg425Cys) single nucleotide variant Conflicting classifications of pathogenicity missense variant Chr10:95621225 rs762742204 .Diagnostics Division, CENTRE FOR DNA FINGERPRINTING AND DIAGNOSTICS
NM_000052.7(ATP7A):c.3547G>A (p.Gly1183Ser) single nucleotide variant Uncertain significance missense variant|non-coding transcript variant ChrX:78038871 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_000052.7(ATP7A):c.1933C>T (p.Arg645Ter) single nucleotide variant Pathogenic nonsense ChrX:78011239 rs72554640 .Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics
NM_016938.5(EFEMP2):c.608A>C (p.Asp203Ala) single nucleotide variant Pathogenic/Likely pathogenic missense variant|non-coding transcript variant Chr11:65869976 rs193302864 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_006329.4(FBLN5):c.1134T>G (p.Tyr378Ter) single nucleotide variant Pathogenic nonsense Chr14:91877538 rs746506432 .Diagnostics Services (NGS), CSIR - Centre For Cellular And Molecular Biology
NM_000158.4(GBE1):c.1459G>T (p.Asp487Tyr) single nucleotide variant Likely pathogenic missense variant Chr3:81578084 rs2106933976 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_001042545.2(LTBP4):c.608T>A (p.Leu203Ter) single nucleotide variant Likely pathogenic nonsense Chr19:40605570 rs2081454038 .Lifecell International Pvt. Ltd
NM_001042545.2(LTBP4):c.1828C>T (p.Gln610Ter) single nucleotide variant Pathogenic nonsense Chr19:40611169 rs1568406407 .Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics
NM_006907.4(PYCR1):c.67+2T>A single nucleotide variant Pathogenic splice donor variant Chr17:81936746 rs2041207320 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India

Graph displaying all Indian institutes, the rare genetic disorders they studied, and the variants submitted to ClinVar