GenTIGSA Gene Database on Rare Genetic Disorders

Variants in ClinVar from 539 of 916 Rare Genetic Disorders of GenTIGS

Charcot-Marie-Tooth disease

An  Autosomal dominant, Autosomal recessive, X-linked recessive, X-linked dominant  mode(s) within the Neuromuscular disorders  category

Benign/Likely benign 1
Conflicting classifications of pathogenicity 8
Likely pathogenic 4
Pathogenic 13
Pathogenic/Likely pathogenic 6
Uncertain significance 6

Variant name Variant type GRCH38 location Germline classification Molecular consequence dbSNP_ID Submitter
NM_001605.3(AARS1):c.580C>T (p.Arg194Trp) Single nucleotide variant Chr16:70271872 Uncertain significance Missense variant rs764675357 .Department of Biochemistry, All India Institute of Medical Sciences, Kalyani
NM_001122955.4(BSCL2):c.461C>T (p.Ser154Leu) Single nucleotide variant Chr11:62702493 Pathogenic/Likely pathogenic Non-coding transcript variant|missense variant rs137852973 .Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics
NM_018706.7(DHTKD1):c.1455T>G (p.Tyr485Ter) Single nucleotide variant Chr10:12097780 Likely pathogenic Nonsense rs606231237 .Lifecell International Pvt. Ltd
NM_001005361.3(DNM2):c.1810G>A (p.Glu604Lys) Single nucleotide variant Chr19:10823816 Conflicting classifications of pathogenicity Missense variant rs951875086 .Diagnostics Services (NGS), CSIR - Centre For Cellular And Molecular Biology
NM_001376.5(DYNC1H1):c.751C>T (p.Arg251Cys) Single nucleotide variant Chr14:101979951 Conflicting classifications of pathogenicity Missense variant rs879253979 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_018972.4(GDAP1):c.358C>T (p.Arg120Trp) Single nucleotide variant Chr8:74360184 Pathogenic Missense variant|intron variant rs104894078 .Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics
NM_001358263.1(HK1):c.19C>T (p.Arg7Ter) Single nucleotide variant Chr10:69288762 Pathogenic/Likely pathogenic Nonsense|5 prime UTR variant rs779250530 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
.Neuberg Centre For Genomic Medicine, NCGM
NM_000188.3(HK1):c.1252A>G (p.Lys418Glu) Single nucleotide variant Chr10:69380082 Likely pathogenic Missense variant rs1564557037 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_001540.5(HSPB1):c.418C>G (p.Arg140Gly) Single nucleotide variant Chr7:76303855 Pathogenic Missense variant rs121909112 .Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics
NM_002180.3(IGHMBP2):c.1591C>A (p.Pro531Thr) Single nucleotide variant Chr11:68934517 Conflicting classifications of pathogenicity Missense variant rs756985703 .Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics
.Lifecell International Pvt. Ltd
.Neuberg Centre For Genomic Medicine, NCGM
NM_022489.4(INF2):c.2507T>C (p.Ile836Thr) Single nucleotide variant Chr14:104712450 Benign/Likely benign Missense variant rs767351070 .Genetic Testing Lab, Ashok and Rita Patel Institute of Integrated Study and Research in Biotechnology and Allied Sciences
NM_001365951.3(KIF1B):c.197G>A (p.Cys66Tyr) Single nucleotide variant Chr1:10258506 Uncertain significance Missense variant .Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics
NM_001365951.3(KIF1B):c.2642A>G (p.Tyr881Cys) Single nucleotide variant Chr1:10324862 Conflicting classifications of pathogenicity Missense variant rs755850268 .Laboratory of Molecular and Cytogenetics, Department of Anatomy, All India Institute of Medical Sciences (AIIMS)
NM_001365951.3(KIF1B):c.4922C>T (p.Ser1641Phe) Single nucleotide variant Chr1:10371238 Uncertain significance Missense variant rs748589511 .Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics
NM_170707.4(LMNA):c.62T>C (p.Leu21Pro) Single nucleotide variant Chr1:156114980 Uncertain significance Missense variant rs1649704361 .Diagnostics Services (NGS), CSIR - Centre For Cellular And Molecular Biology
NM_170707.4(LMNA):c.91_93del (p.Glu31del) Deletion Chr1:156115007 - 156115009 Pathogenic Inframe_deletion rs864309525 .Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics
NM_170707.4(LMNA):c.1157G>A (p.Arg386Lys) Single nucleotide variant Chr1:156136121 Pathogenic Missense variant rs267607545 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_170707.4(LMNA):c.1824C>T (p.Gly608=) Single nucleotide variant Chr1:156138613 Pathogenic Synonymous variant|intron variant rs58596362 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_170707.4(LMNA):c.1579C>T (p.Arg527Cys) Single nucleotide variant Chr1:156137203 Conflicting classifications of pathogenicity Missense variant rs57318642 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_001005373.4(LRSAM1):c.2111G>T (p.Arg704Leu) Single nucleotide variant Chr9:127502838 Uncertain significance Missense variant|non-coding transcript variant rs140808447 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_014874.4(MFN2):c.724C>T (p.His242Tyr) Single nucleotide variant Chr1:11999003 Likely pathogenic Missense variant rs2523036866 .Division of Medical Genetics, Department of Pediatrics, All India Institute of Medical Sciences, New Delhi
NM_014874.4(MFN2):c.314C>T (p.Thr105Met) Single nucleotide variant Chr1:11996158 Pathogenic/Likely pathogenic Missense variant rs863224069 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
.Neuberg Centre For Genomic Medicine, NCGM
NM_001303256.3(MORC2):c.1220G>T (p.Cys407Phe) Single nucleotide variant Chr22:30937964 Uncertain significance Missense variant rs1555938741 .Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics
NM_016156.6(MTMR2):c.304C>T (p.Arg102Ter) Single nucleotide variant Chr11:95862325 Pathogenic Nonsense rs115506357 .Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics
NM_000263.4(NAGLU):c.384-3C>A Single nucleotide variant Chr17:42537395 Conflicting classifications of pathogenicity Intron variant rs1216280532 .Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics
.Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_000263.4(NAGLU):c.1444C>T (p.Arg482Trp) Single nucleotide variant Chr17:42543450 Pathogenic Missense variant rs104894596 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
.Neuberg Centre For Genomic Medicine, NCGM
NM_006096.4(NDRG1):c.537+2_537+10del Deletion Chr8:133256767 - 133256775 Pathogenic Inframe_deletion|splice donor variant rs2130719557 .Institute of Bioinformatics
NM_024577.4(SH3TC2):c.289G>A (p.Ala97Thr) Single nucleotide variant Chr5:149044629 Conflicting classifications of pathogenicity Missense variant rs562689036 .Diagnostics Services (NGS), CSIR - Centre For Cellular And Molecular Biology
NM_024577.4(SH3TC2):c.1942C>T (p.Arg648Trp) Single nucleotide variant Chr5:149027790 Conflicting classifications of pathogenicity Missense variant rs537049075 .Diagnostics Services (NGS), CSIR - Centre For Cellular And Molecular Biology
NM_024577.4(SH3TC2):c.3325C>T (p.Arg1109Ter) Single nucleotide variant Chr5:149010272 Pathogenic Nonsense rs80338934 .Institute of Medical Genetics and Genomics, Sir Ganga Ram Hospital
.Neuberg Centre For Genomic Medicine, NCGM
NM_025137.4(SPG11):c.2716del (p.Gln906fs) Deletion Chr15:44620308 Pathogenic Frameshift variant rs312262747 .Lifecell International Pvt. Ltd
.Neuberg Centre For Genomic Medicine, NCGM
NM_025137.4(SPG11):c.2146C>T (p.Gln716Ter) Single nucleotide variant Chr15:44626429 Pathogenic/Likely pathogenic Nonsense rs312262737 .Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics
.Neuberg Centre For Genomic Medicine, NCGM
NM_025137.4(SPG11):c.733_734del (p.Met245fs) Deletion Chr15:44657230 - 44657231 Pathogenic Frameshift variant rs312262720 .Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics
.Neuberg Centre For Genomic Medicine, NCGM
NM_003172.4(SURF1):c.535dup (p.Arg179fs) Duplication Chr9:133352746 - 133352747 Pathogenic/Likely pathogenic Frameshift variant rs1836465016 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_021625.5(TRPV4):c.1219A>G (p.Lys407Glu) Single nucleotide variant Chr12:109796638 Pathogenic Missense variant|intron variant rs515726153 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_021625.5(TRPV4):c.2389G>A (p.Glu797Lys) Single nucleotide variant Chr12:109784385 Pathogenic Missense variant rs267607149 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
.Neuberg Centre For Genomic Medicine, NCGM
NM_021625.5(TRPV4):c.1781G>A (p.Arg594His) Single nucleotide variant Chr12:109792695 Pathogenic/Likely pathogenic Missense variant rs77975504 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_007126.5(VCP):c.553G>A (p.Glu185Lys) Single nucleotide variant Chr9:35065274 Likely pathogenic Missense variant rs864309501 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India

Indian Institutes & Variant Submission Overview
Chromosome-wise Variant Distribution