GenTIGSA Gene Database on Rare Genetic Disorders

Variants in ClinVar from 539 of 916 Rare Genetic Disorders of GenTIGS

Autosomal recessive congenital ichthyosis 4B

An  Autosomal recessive  mode(s) within the Skin disorders  category

Likely pathogenic 2
Pathogenic 2
Pathogenic/Likely pathogenic 1

Variant name Variant type GRCH38 location Germline classification Molecular consequence dbSNP_ID Submitter
NM_173076.3(ABCA12):c.5878C>T (p.Arg1960Ter) Single nucleotide variant Chr2:214966854 Likely pathogenic Nonsense|non-coding transcript variant rs769753487 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_173076.3(ABCA12):c.7344-1G>C Single nucleotide variant Chr2:214943018 Pathogenic Splice acceptor variant rs2105917562 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_173076.3(ABCA12):c.3882G>A (p.Trp1294Ter) Single nucleotide variant Chr2:214987741 Pathogenic/Likely pathogenic Nonsense|non-coding transcript variant rs1452228678 .Lifecell International Pvt. Ltd
.Neuberg Centre For Genomic Medicine, NCGM
NM_173076.3(ABCA12):c.5939+4A>G Single nucleotide variant Chr2:214959020 Likely pathogenic Intron variant rs1131692156 .Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics
NM_173076.3(ABCA12):c.859C>T (p.Arg287Ter) Single nucleotide variant Chr2:215045850 Pathogenic Nonsense|non-coding transcript variant rs11891778 .Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics

Indian Institutes & Variant Submission Overview
Chromosome-wise Variant Distribution