GenTIGSA Gene Database on Rare Genetic Disorders

Variants in ClinVar from 539 of 916 Rare Genetic Disorders of GenTIGS

Atelosteogenesis type II

An  Autosomal recessive  mode(s) within the Bone disorders  category

Likely pathogenic 1
Pathogenic 3
Pathogenic/Likely pathogenic 1

Variant name Variant type GRCH38 location Germline classification Molecular consequence dbSNP_ID Submitter
NM_000112.4(SLC26A2):c.796dup (p.Thr266fs) Duplication Chr5:149980388 - 149980389 Pathogenic Frameshift variant rs767996373 .Institute of Medical Genetics and Genomics, Sir Ganga Ram Hospital
NM_000112.4(SLC26A2):c.1382C>T (p.Ala461Val) Single nucleotide variant Chr5:149980975 Likely pathogenic Missense variant rs2113698650 .Institute of Medical Genetics and Genomics, Sir Ganga Ram Hospital
NM_000112.4(SLC26A2):c.532C>T (p.Arg178Ter) Single nucleotide variant Chr5:149978184 Pathogenic Nonsense rs104893919 .Diagnostics Division, CENTRE FOR DNA FINGERPRINTING AND DIAGNOSTICS
.Institute of Medical Genetics and Genomics, Sir Ganga Ram Hospital
NM_000112.4(SLC26A2):c.835C>T (p.Arg279Trp) Single nucleotide variant Chr5:149980428 Pathogenic/Likely pathogenic Missense variant rs104893915 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_000112.4(SLC26A2):c.1724del (p.Lys575fs) Deletion Chr5:149981316 Pathogenic Frameshift variant rs386833498 .Institute of Medical Genetics and Genomics, Sir Ganga Ram Hospital

Indian Institutes & Variant Submission Overview
Chromosome-wise Variant Distribution