GenTIGSA Gene Database on Rare Genetic Disorders

Variants in ClinVar from 539 of 916 Rare Genetic Disorders of GenTIGS

Achondrogenesis

An  Autosomal dominant, Autosomal recessive  mode(s) within the Bone disorders  category

Conflicting classifications of pathogenicity 1
Likely pathogenic 6
Pathogenic 6
Pathogenic/Likely pathogenic 2

Variant name Variant type GRCH38 location Germline classification Molecular consequence dbSNP_ID Submitter
NM_001844.5(COL2A1):c.2744G>A (p.Gly915Glu) Single nucleotide variant Chr12:47978748 Likely pathogenic Missense variant .Department of Medical Genetics, Sanjay Gandhi Post Graduate Institute of Medical Sciences
NM_001844.5(COL2A1):c.1952G>T (p.Gly651Val) Single nucleotide variant Chr12:47983726 Likely pathogenic Missense variant rs1447463543 .Institute of Medical Genetics and Genomics, Sir Ganga Ram Hospital
NM_001844.5(COL2A1):c.2995G>T (p.Gly999Cys) Single nucleotide variant Chr12:47978299 Likely pathogenic Missense variant rs2136526244 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_001844.5(COL2A1):c.2114G>A (p.Gly705Asp) Single nucleotide variant Chr12:47982927 Likely pathogenic Missense variant rs2136551606 .Institute of Medical Genetics and Genomics, Sir Ganga Ram Hospital
NM_001844.5(COL2A1):c.1232G>A (p.Gly411Glu) Single nucleotide variant Chr12:47987303 Likely pathogenic Missense variant rs2136577158 .Institute of Medical Genetics and Genomics, Sir Ganga Ram Hospital
NM_001844.5(COL2A1):c.3121G>A (p.Gly1041Ser) Single nucleotide variant Chr12:47977644 Pathogenic Missense variant rs2136522964 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_001844.5(COL2A1):c.4135C>T (p.Arg1379Cys) Single nucleotide variant Chr12:47974271 Conflicting classifications of pathogenicity Missense variant rs141951587 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_001844.5(COL2A1):c.2965C>T (p.Arg989Cys) Single nucleotide variant Chr12:47978329 Pathogenic/Likely pathogenic Missense variant rs121912874 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
.Suma Genomics
NM_000112.4(SLC26A2):c.796dup (p.Thr266fs) Duplication Chr5:149980388 - 149980389 Pathogenic Frameshift variant rs767996373 .Institute of Medical Genetics and Genomics, Sir Ganga Ram Hospital
NM_000112.4(SLC26A2):c.532C>T (p.Arg178Ter) Single nucleotide variant Chr5:149978184 Pathogenic Nonsense rs104893919 .Diagnostics Division, CENTRE FOR DNA FINGERPRINTING AND DIAGNOSTICS
.Institute of Medical Genetics and Genomics, Sir Ganga Ram Hospital
NM_000112.4(SLC26A2):c.835C>T (p.Arg279Trp) Single nucleotide variant Chr5:149980428 Pathogenic/Likely pathogenic Missense variant rs104893915 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_000112.4(SLC26A2):c.1724del (p.Lys575fs) Deletion Chr5:149981316 Pathogenic Frameshift variant rs386833498 .Institute of Medical Genetics and Genomics, Sir Ganga Ram Hospital
NM_004239.4(TRIP11):c.1107_1108dup (p.Thr370fs) Duplication Chr14:92014292 - 92014293 Likely pathogenic Frameshift variant rs2140129581 .Institute of Medical Genetics and Genomics, Sir Ganga Ram Hospital
NM_004239.4(TRIP11):c.526C>T (p.Arg176Ter) Single nucleotide variant Chr14:92021618 Pathogenic Nonsense rs758589172 .Institute of Medical Genetics and Genomics, Sir Ganga Ram Hospital
NM_004239.4(TRIP11):c.5457+81T>A Single nucleotide variant Chr14:91975091 Pathogenic Intron variant rs2056447170 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India

Indian Institutes & Variant Submission Overview
Chromosome-wise Variant Distribution