GenTIGSA Gene Database on Rare Genetic Disorders

Lists of Rare Genetic Disorders  

Renal Tubular Dysgenesis(Allanson Pantzar McLeod syndrome) 
An Autosomal recessive mode(s) within the Nephrological disorders category
Reported Pathogenic variants
Candidate Gene Information
S.No. Name/GeneID Description Cytogentic Band Gene Location on genomic DNA Gene Length Exons Details Gene Cross-References
1 REN/5972 renin 1q32.1 Chr1, NC_000001.11
(204154819..204166337, complement)
11519 nt 10 More... OMIM gene
gnomAD browser
EnsEMBL
GeneCards
ClinGen gene

2 ACE/1636 angiotensin I converting enzyme 17q23.3 Chr17, NC_000017.11
(63477061..63498373)
21313 nt 26 More... OMIM gene
gnomAD browser
EnsEMBL
GeneCards
ClinGen gene

3 AGTR1/185 angiotensin II receptor type 1 3q24 Chr3, NC_000003.12
(148697903..148743003)
45101 nt 5 More... OMIM gene
gnomAD browser
EnsEMBL
GeneCards
ClinGen gene

4 AGT/183 angiotensinogen 1q42.2 Chr1, NC_000001.11
(230702523..230745583, complement)
43061 nt 6 More... OMIM gene
gnomAD browser
EnsEMBL
GeneCards
ClinGen gene

5 EBF3/253738 EBF transcription factor 3 10q26.3 Chr10, NC_000010.11
(129835233..129964274, complement)
129042 nt 19 More... OMIM gene
gnomAD browser
EnsEMBL
GeneCards
ClinGen gene

Variant Information             Highlighted rows indicate variants are reported from India
Disorder Cross-References:      Orphanet                    GTR          MedGen          MalaCards          EMBL-EBI OLS    Monarch Initiative          Human Phenotype Ontology          NORD     

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