GenTIGSA Gene Database on Rare Genetic Disorders

Lists of Rare Genetic Disorders  

L-2-hydroxyglutaric Aciduria(L2HGA)      Explore Disorder's Alias
An Autosomal recessive mode(s) within the Metabolic disorders category
Reported Pathogenic variants
Candidate Gene Information
S.No. Name/GeneID Description Cytogentic Band Gene Location on genomic DNA Gene Length Exons Details Gene Cross-References
1 L2HGDH/79944 L-2-hydroxyglutarate dehydrogenase 14q21.3 Chr14, NC_000014.9
(50242434..50312229, complement)
69796 nt 15 More... OMIM gene
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Disorder Cross-References:      Orphanet          OMIM          GARD          GTR          MedGen          MalaCards          EMBL-EBI OLS    Monarch Initiative          Human Phenotype Ontology          NORD     

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