GenTIGSA Gene Database on Rare Genetic Disorders

Lists of Rare Genetic Disorders  

Hyperinsulinemic Hypoglycemia, Familial, 1(Congenital isolated hyperinsulinism) 
An Autosomal dominant, Autosomal recessive mode(s) within the Metabolic disorders category
Reported Pathogenic variants
Candidate Gene Information
S.No. Name/GeneID Description Cytogentic Band Gene Location on genomic DNA Gene Length Exons Details Gene Cross-References
1 ABCC8/6833 ATP binding cassette subfamily C member 8 11p15.1 Chr11, NC_000011.10
(17392498..17476845, complement)
84348 nt 38 More... OMIM gene
gnomAD browser
EnsEMBL
GeneCards
ClinGen gene

Variant Information    
Disorder Cross-References:      Orphanet          OMIM                    GTR          MedGen          MalaCards          EMBL-EBI OLS    Monarch Initiative          NORD     

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Clinical Symptoms & Disabilities