GenTIGSA Gene Database on Rare Genetic Disorders

Lists of Rare Genetic Disorders  

Histiocytic Medullary Reticulosis(Omenn syndrome)      Explore Disorder's Alias
An Autosomal recessive mode(s) within the Cancer disorders category
Reported Pathogenic variants
Candidate Gene Information
S.No. Name/GeneID Description Cytogentic Band Gene Location on genomic DNA Gene Length Exons Details Gene Cross-References
1 DCLRE1C/64421 DNA cross-link repair 1C 10p13 Chr10, NC_000010.11
(14897359..14954432, complement)
57074 nt 20 More... OMIM gene
gnomAD browser
EnsEMBL
GeneCards
ClinGen gene

2 RAG2/5897 recombination activating 2 11p12 Chr11, NC_000011.10
(36590996..36598236, complement)
7241 nt 2 More... OMIM gene
gnomAD browser
EnsEMBL
GeneCards
ClinGen gene

3 RAG1/5896 recombination activating 1 11p12 Chr11, NC_000011.10
(36510353..36579762)
69410 nt 7 More... OMIM gene
gnomAD browser
EnsEMBL
GeneCards
ClinGen gene

4 IL7R/3575 interleukin 7 receptor 5p13.2 Chr5, NC_000005.10
(35856891..35879603)
22713 nt 8 More... OMIM gene
gnomAD browser
EnsEMBL
GeneCards
ClinGen gene

Variant Information    
Disorder Cross-References:      Orphanet          OMIM          GARD          GTR          MedGen          MalaCards          EMBL-EBI OLS    Monarch Initiative          NORD     

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