GenTIGSA Gene Database on Rare Genetic Disorders
  Beta Version

Lists of Rare Genetic Disorders  

Cornelia De Lange Syndrome 1(NIPBL-Related Cornelia de Lange Syndrome)      Explore Disorder's Alias
An Autosomal dominant mode(s) within the Multisystemic disorders category
Reported Pathogenic variants
Candidate Gene Information
S.No. Name/GeneID Description Cytogentic Band Gene Location on genomic DNA Gene Length Exons Details Gene Cross-References
1 NIPBL/25836 NIPBL cohesin loading factor 5p13.2 Chr5, NC_000005.10
(36876769..37066413)
189645 nt 48 More... OMIM gene
gnomAD browser
EnsEMBL
GeneCards
ClinGen gene

2 TAF6/6878 TATA-box binding protein associated factor 6 7q22.1 Chr7, NC_000007.14
(100107070..100127171, complement)
20102 nt 20 More... OMIM gene
gnomAD browser
EnsEMBL
GeneCards
ClinGen gene

3 KMT2A/4297 lysine methyltransferase 2A 11q23.3 Chr11, NC_000011.10
(118436492..118526832)
90341 nt 37 More... OMIM gene
gnomAD browser
EnsEMBL
GeneCards
ClinGen gene

4 HDAC8/55869 histone deacetylase 8 Xq13.1 ChrX, NC_000023.11
(72329516..72572843, complement)
243328 nt 17 More... OMIM gene
gnomAD browser
EnsEMBL
GeneCards
ClinGen gene

5 SMC3/9126 structural maintenance of chromosomes 3 10q25.2 Chr10, NC_000010.11
(110567695..110606048)
38354 nt 29 More... OMIM gene
gnomAD browser
EnsEMBL
GeneCards
ClinGen gene

6 RAD21/5885 RAD21 cohesin complex component 8q24.11 Chr8, NC_000008.11
(116845934..116874776, complement)
28843 nt 14 More... OMIM gene
gnomAD browser
EnsEMBL
GeneCards
ClinGen gene

Variant Information             Highlighted rows indicate variants are reported from India
Disorder Cross-References:      Orphanet          OMIM          GARD          GTR          MedGen          MalaCards          EMBL-EBI OLS    Monarch Initiative          NORD     

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