GenTIGSA Gene Database on Rare Genetic Disorders
  Beta Version

Lists of Rare Genetic Disorders  

Congenital Stationary Night Blindness(Early-onset non-progressive night blindness)      Explore Disorder's Alias
An Autosomal dominant, Autosomal recessive, X-linked recessive mode(s) within the Eye disorders category
Reported Pathogenic variants
Candidate Gene Information
S.No. Name/GeneID Description Cytogentic Band Gene Location on genomic DNA Gene Length Exons Details Gene Cross-References
1 GRM6/2916 glutamate metabotropic receptor 6 5q35.3 Chr5, NC_000005.10
(178978327..178995320, complement)
16994 nt 11 More... OMIM gene
gnomAD browser
EnsEMBL
GeneCards
ClinGen gene

2 TRPM1/4308 transient receptor potential cation channel subfamily M member 1 15q13.3 Chr15, NC_000015.10
(31001065..31161160, complement)
160096 nt 29 More... OMIM gene
gnomAD browser
EnsEMBL
GeneCards
ClinGen gene

3 NYX/60506 nyctalopin Xp11.4 ChrX, NC_000023.11
(41447343..41475652)
28310 nt 2 More... OMIM gene
gnomAD browser
EnsEMBL
GeneCards
ClinGen gene

4 CACNA1F/778 calcium voltage-gated channel subunit alpha1 F Xp11.23 ChrX, NC_000023.11
(49205063..49233340, complement)
28278 nt 48 More... OMIM gene
gnomAD browser
EnsEMBL
GeneCards
ClinGen gene

5 RHO/6010 rhodopsin 3q22.1 Chr3, NC_000003.12
(129528639..129535344)
6706 nt 5 More... OMIM gene
gnomAD browser
EnsEMBL
GeneCards
ClinGen gene

6 PDE6B/5158 phosphodiesterase 6B 4p16.3 Chr4, NC_000004.12
(625573..670782)
45210 nt 23 More... OMIM gene
gnomAD browser
EnsEMBL
GeneCards
ClinGen gene

7 GNAT1/2779 G protein subunit alpha transducin 1 3p21.31 Chr3, NC_000003.12
(50191610..50197696)
6087 nt 9 More... OMIM gene
gnomAD browser
EnsEMBL
GeneCards
ClinGen gene

8 SLC24A1/9187 solute carrier family 24 member 1 15q22.31 Chr15, NC_000015.10
(65611350..65661002)
49653 nt 16 More... OMIM gene
gnomAD browser
EnsEMBL
GeneCards
ClinGen gene

9 GPR179/440435 G protein-coupled receptor 179 17q12 Chr17, NC_000017.11
(38324571..38343956, complement)
19386 nt 11 More... OMIM gene
gnomAD browser
EnsEMBL
GeneCards
ClinGen gene

10 LRIT3/345193 leucine rich repeat, Ig-like and transmembrane domains 3 4q25 Chr4, NC_000004.12
(109848107..109872315)
24209 nt 5 More... OMIM gene
gnomAD browser
EnsEMBL
GeneCards
ClinGen gene

11 GNB3/2784 G protein subunit beta 3 12p13.31 Chr12, NC_000012.12
(6840925..6847393)
6469 nt 8 More... OMIM gene
gnomAD browser
EnsEMBL
GeneCards
ClinGen gene

12 ABCA4/24 ATP binding cassette subfamily A member 4 1p22.1 Chr1, NC_000001.11
(93992834..94121148, complement)
128315 nt 50 More... OMIM gene
gnomAD browser
EnsEMBL
GeneCards
ClinGen gene

13 RPGR/6103 retinitis pigmentosa GTPase regulator Xp11.4 ChrX, NC_000023.11
(38269163..38327509, complement)
58347 nt 25 More... OMIM gene
gnomAD browser
EnsEMBL
GeneCards
ClinGen gene

14 GRK1/6011 G protein-coupled receptor kinase 1 13q34 Chr13, NC_000013.11
(113648199..113737736)
89538 nt 8 More... OMIM gene
gnomAD browser
EnsEMBL
GeneCards
ClinGen gene

Variant Information             Highlighted rows indicate variants are reported from India
Disorder Cross-References:      Orphanet          OMIM          GARD          GTR          MedGen          MalaCards          EMBL-EBI OLS    Monarch Initiative          Human Phenotype Ontology          NORD     

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