GenTIGSA Gene Database on Rare Genetic Disorders
  Beta Version

Lists of Rare Genetic Disorders  

Autosomal Recessive Nonsyndromic Hearing Loss 9(OTOF-related hearing loss) 
An Autosomal recessive mode(s) within the Ear disorders category
Reported Pathogenic variants
Candidate Gene Information
S.No. Name/GeneID Description Cytogentic Band Gene Location on genomic DNA Gene Length Exons Details Gene Cross-References
1 OTOF/9381 otoferlin 2p23.3 Chr2, NC_000002.12
(26457203..26558756, complement)
101554 nt 48 More... OMIM gene
gnomAD browser
EnsEMBL
GeneCards
ClinGen gene

2 SERPINB6/5269 serpin family B member 6 6p25.2 Chr6, NC_000006.12
(2948159..2971793, complement)
23635 nt 12 More... OMIM gene
gnomAD browser
EnsEMBL
GeneCards
ClinGen gene

3 TSPEAR/54084 thrombospondin type laminin G domain and EAR repeats 21q22.3 Chr21, NC_000021.9
(44497893..44711572, complement)
213680 nt 13 More... OMIM gene
gnomAD browser
EnsEMBL
GeneCards
ClinGen gene

4 CABP2/51475 calcium binding protein 2 11q13.2 Chr11, NC_000011.10
(67518912..67523446, complement)
4535 nt 7 More... OMIM gene
gnomAD browser
EnsEMBL
GeneCards
ClinGen gene

Variant Information             Highlighted rows indicate variants are reported from India
Disorder Cross-References:      Orphanet          OMIM                    GTR          MedGen          MalaCards          EMBL-EBI OLS    Monarch Initiative          NORD     

Patient care services
Clinical Symptoms & Disabilities