GenTIGSA Gene Database on Rare Genetic Disorders

Lists of Rare Genetic Disorders  

Arthrogryposis, Renal Dysfunction, And Cholestasis 1(ARCS1)      Explore Disorder's Alias
An Autosomal recessive mode(s) within the Multisystemic disorders category
Reported Pathogenic variants
Candidate Gene Information
S.No. Name/GeneID Description Cytogentic Band Gene Location on genomic DNA Gene Length Exons Details Gene Cross-References
1 VPS33B/26276 VPS33B late endosome and lysosome associated 15q26.1 Chr15, NC_000015.10
(90998416..91022621, complement)
24206 nt 24 More... OMIM gene
gnomAD browser
EnsEMBL
GeneCards
ClinGen gene

2 VIPAS39/63894 VPS33B interacting protein, apical-basolateral polarity regulator, spe-39 homolog 14q24.3 Chr14, NC_000014.9
(77426675..77457601, complement)
30927 nt 22 More... OMIM gene
gnomAD browser
EnsEMBL
GeneCards
ClinGen gene

3 FBN1/2200 fibrillin 1 15q21.1 Chr15, NC_000015.10
(48408313..48645709, complement)
237397 nt 68 More... OMIM gene
gnomAD browser
EnsEMBL
GeneCards
ClinGen gene

4 CPAP/55835 centrosome assembly and centriole elongation protein 13q12.13 Chr13, NC_000013.11
(24882279..24934000, complement)
51722 nt 24 More... OMIM gene
gnomAD browser
EnsEMBL
GeneCards
ClinGen gene

Variant Information    
Disorder Cross-References:      Orphanet          OMIM          GARD          GTR          MedGen          MalaCards          EMBL-EBI OLS    Monarch Initiative          NORD     

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