GenTIGSA Gene Database on Rare Genetic Disorders

Lists of Rare Genetic Disorders  

3-methylglutaconic Aciduria Type 1(3-methylglutaconic aciduria caused by mutation in auh)      Explore Disorder's Alias
An Autosomal recessive mode(s) within the Metabolic disorders category
Reported Pathogenic variants
Candidate Gene Information
S.No. Name/GeneID Description Cytogentic Band Gene Location on genomic DNA Gene Length Exons Details Gene Cross-References
1 AUH/549 AU RNA binding methylglutaconyl-CoA hydratase 9q22.31 Chr9, NC_000009.12
(91213823..91361918, complement)
148096 nt 20 More... OMIM gene
gnomAD browser
EnsEMBL
GeneCards
ClinGen gene

Variant Information    
Disorder Cross-References:      Orphanet          OMIM          GARD          GTR          MedGen          MalaCards          EMBL-EBI OLS    Monarch Initiative          NORD     

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