GenTIGSA Gene Database on Rare Genetic Disorders
  Beta Version

Lists of Rare Genetic Disorders  

3-methylcrotonyl-CoA Carboxylase 1 Deficiency(3 Alpha methylcrotonylglycinuria 1)      Explore Disorder's Alias
An Autosomal recessive mode(s) within the Metabolic disorders category
Reported Pathogenic variants
Candidate Gene Information
S.No. Name/GeneID Description Cytogentic Band Gene Location on genomic DNA Gene Length Exons Details Gene Cross-References
1 MCCC1/56922 methylcrotonyl-CoA carboxylase subunit 1 3q27.1 Chr3, NC_000003.12
(183015218..183116196, complement)
100979 nt 23 More... OMIM gene
gnomAD browser
EnsEMBL
GeneCards
ClinGen gene

Variant Information             Highlighted rows indicate variants are reported from India
Disorder Cross-References:      Orphanet          OMIM          GARD          GTR          MedGen          MalaCards          EMBL-EBI OLS    Monarch Initiative          NORD     

Patient care services
Clinical Symptoms & Disabilities