GenTIGSA Gene Database on Rare Genetic Disorders

Lists of Rare Genetic Disorders  

3 Beta-Hydroxysteroid Dehydrogenase Deficiency(Congenital adrenal hyperplasia due to 3-beta-hydroxysteroid dehydrogenase deficiency)      Explore Disorder's Alias
An Autosomal recessive mode(s) within the Endocrine disorders category
Reported Pathogenic variants
Candidate Gene Information
S.No. Name/GeneID Description Cytogentic Band Gene Location on genomic DNA Gene Length Exons Details Gene Cross-References
1 HSD3B2/3284 hydroxy-delta-5-steroid dehydrogenase, 3 beta- and steroid delta-isomerase 2 1p12 Chr1, NC_000001.11
(119414931..119423034)
8104 nt 5 More... OMIM gene
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Variant Information    
Disorder Cross-References:      Orphanet          OMIM          GARD          GTR          MedGen          MalaCards          EMBL-EBI OLS    Monarch Initiative          NORD     

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