GenTIGSA Gene Database on Rare Genetic Disorders
X-linked Lymphoproliferative Disease Due To SH2D1A Deficiency  
Disease Aliases (10)

Ebv infection severe susceptibility to

Epstein barr virus infection familial fatal

Immunodeficiency 5

Immunodeficiency, x-linked progressive combined variable

Infectious mononucleosis, severe, susceptibility to

Lymphoproliferative syndrome, x-linked, 1, x-linked recessive

Sap deficiency

Sh2d1a-related lymphoproliferative disease, x-linked

Sh2d1a/slam-associated protein deficiency

X-linked lymphoproliferative syndrome type 1

Associated Genes (0)
 

Cross-references of X-linked lymphoproliferative disease due to SH2D1A deficiency OMIM GARD Orphanet NCBI-GTR NCBI-MedGen MalaCards      MeSH Annotations