GenTIGSA Gene Database on Rare Genetic Disorders
Sponastrime Dysplasia  
Disease Aliases (12)

Semdsp

Short-limb dwarfism with saddle nose, spinal alterations, and metaphyseal striation

Sponastrime dysplasia

Spondylar and nasal alterations with striated metaphyses

Short limb dwarfism with saddle nose, spinal alterations, and metaphyseal striation

Sponastrime type

Spondylar and nasal alterations-striated metaphyses syndrome

Spondylar and nasal changes with striations of the metaphyses (sponastrime) dysplasia

Spondyloepimetaphyseal dysplasia

Spondyloepimetaphyseal dysplasia sponastrime type

Spondyloepimetaphyseal dysplasia, sponastrime type

Spondylar and nasal changes with triations of the metaphyses (sponastrime) dysplasia

Associated Genes (1)
 

NCBI-RefSeq:  TONSL   (Tonsoku like, DNA repair protein)

External Links:  gnomAD browser   Ensembl   GeneCards

 


Cross-references of Sponastrime dysplasia OMIM GARD Orphanet NCBI-GTR NCBI-MedGen MalaCards      MeSH Annotations