GenTIGSA Gene Database on Rare Genetic Disorders
Roberts-SC Phocomelia Syndrome  
Disease Aliases (19)

Appelt-gerken-lenz syndrome

Hypomelia hypotrichosis facial hemangioma syndrome

Hypomelia-hypotrichosis-facial hemangioma syndrome

Long bone deficiencies associated with cleft lip-palate

Pseudothalidomide syndrome

Rbs

Roberts syndrome

Roberts syndrome; rbs

Robert's syndrome

Roberts syndrome/sc phocomelia

Roberts tetraphocomelia syndrome

Roberts-sc phocomelia syndrome

Sc pseudothalidomide syndrome

Sc phocomelia syndrome (mild variant of roberts syndrome)

Sc syndrome

Tetraphocomelia-cleft palate syndrome

Phocomelia-pseudothalidomide syndrome

Associated Genes (1)
 

NCBI-RefSeq:  ESCO2   (Establishment of sister chromatid cohesion N-acetyltransferase 2)

External Links:  gnomAD browser   Ensembl   GeneCards

 


Cross-references of Roberts-SC phocomelia syndrome OMIM GARD Orphanet NCBI-GTR NCBI-MedGen MalaCards      MeSH Annotations