GenTIGSA Gene Database on Rare Genetic Disorders
Polyglandular Autoimmune Syndrome, Type 1  
Disease Aliases (73)

Aire deficiencies

Aire deficiency

Aire autoimmune polyendocrinopathy

Apeced

Apeced - autoimmune polyendocrinopathy-candidiasis-ectodermal dystrophy

Apeced syndrome

Apeded

Aps 1

Aps i

Aps type 1

Aps1

Autoimmune polyendocrine syndrome, type i, with or without reversible metaphyseal dysplasia

Autoimmune polyendocrinopathy syndrome, type i, autosomal dominant

Autoimmune polyendocrinopathy-candidiasis-ectodermal dystrophy

Autoimmune polyglandular syndrome, type i

Autoimmune polyendocrinopathy candidiasis ectodermal dystrophy

Autoimmune polyendocrinopathy syndrome type 1

Autoimmune polyendocrinopathy syndrome, type i, with reversible metaphyseal dysplasia

Autoimmune polyendocrinopathy with candidiasis and ectodermal dystrophy

Autoimmune polyendocrinopathy-candidiasis-ectodermal-dystrophy

Autoimmune polyglandular syndrome i

Autoimmune polyglandular syndrome type i

Autoimmune syndrome type i, polyglandular

Autoimmune hypoparathyroidism - chronic candidiasis - addison's disease

Autoimmune hypoparathyroidism - chronic candidosis - addison's disease

Autoimmune hypoparathyroidism-chronic candidiasis-addison disease syndrome

Autoimmune polyendocrine syndrome type 1

Autoimmune polyendocrine syndrome, type 1

Autoimmune polyendocrinopathy - candidiasis - ectodermal dystrophy syndrome

Autoimmune polyendocrinopathy - candidosis - ectodermal dystrophy syndrome

Autoimmune polyendocrinopathy syndrome, type 1

Autoimmune polyendocrinopathy syndrome, type i

Autoimmune polyendocrinopathy, candidosis and ectodermal dystrophy

Autoimmune polyendocrinopathy-candidiasis-ectodermal dystrophy (apeced)

Autoimmune polyendocrinopathy-candidiasis-ectodermal dystrophy syndrome

Autoimmune polyglandular syndrome type 1

Blizzard syndrome

Candidiasis-endocrinopathy syndrome

Deficiency, aire

Ham syndrome

Hypoadrenocorticism with hypoparathyroidism and superficial moniliasis

Hypoadrenocorticism, hypoparathyroidism and superficial moniliasis

Hypoparathyroidism - addison's disease - mucocutaneous candidiasis

Hypoparathyroidism - addison's disease - mucocutaneous candidosis

Hypoparathyroidism, addison's disease and moniliasis

Hypoparathyroidism-addison disease-mucocutaneous candidiasis syndrome

Juvenile familial endocrinopathy

Medac syndrome

Multiple endocrine deficiency - addison's disease - candidiasis

Multiple endocrine deficiency - addison's disease - candidosis

Multiple endocrine deficiency-addison disease-candidiasis syndrome

Pga 1

Pga i

Pga-i

Polyglandular autoimmune syndrome, type i

Polyglandular deficiency syndrome, persian-jewish type

Polyendocrinopathy candidiasis ectodermal dystrophy, autoimmune

Polyendocrinopathy-candidiasis-ectodermal dystrophy, autoimmune

Polyendocrinopathy-candidiasis-ectodermal-dystrophy, autoimmune

Polyglandular type i autoimmune syndrome

Polyglandular autoimmune syndrome - type 1

Polyglandular autoimmune syndrome type 1

Polyglandular deficiency associated with mucocutaneous candidiasis

Type 1 polyendocrine autoimmunity syndrome

Type i polyglandular autoimmune syndrome

Whitaker syndrom

Whitaker syndrome

Autoimmune polyendocrine syndrome, type i, with or without reversible metaphyseal dysplasia; aps1

Autoimmune polyendocrinopathy caused by mutation in aire

Autoimmune polyendocrinopathy type 1

Autoimmune polyglandular syndrome, type 1

Autoimmune-poly-endocrinopathy-candidiasis-ectodermal-dystrophy syndrome

Polyglandular autoimmune syndrome, type 1

Associated Genes (1)
 

NCBI-RefSeq:  AIRE   (Autoimmune regulator)

External Links:  gnomAD browser   Ensembl   GeneCards

 


Cross-references of Polyglandular autoimmune syndrome, type 1 OMIM GARD Orphanet NCBI-GTR NCBI-MedGen MalaCards      MeSH Annotations