GenTIGSA Gene Database on Rare Genetic Disorders
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Mitochondrial DNA Depletion Syndrome 13  
Disease Aliases (20)

Bxl4-related early-onset mitochondrial encephalopathy

Encephalomyopathic mitochondrial dna depletion syndrome-13

F-box and leucine rich repeat protein 4 related mitochondrial deoxyribonucleic acid depletion syndrome encephalomyopathic form

Fbxl4 (f-box and leucine rich repeat protein 4) related early onset mitochondrial encephalopathy

Fbxl4 deficiency

Fbxl4 mitochondrial dna depletion syndrome

Fbxl4-related early onset mitochondrial encephalopathy

Fbxl4-related encephalomyopathic mitochondrial dna depletion syndrome

Mtdps13

Mitochondrial dna depletion syndrome 13 (encephalomyopathic type)

Mitochondrial dna depletion syndrome 13 encephalomyopathic type

Mitochondrial dna depletion syndrome, encephalomyopathic form with variable craniofacial anomalies

Encephalomyopathic form with variable craniofacial anomalies

Mitochondrial dna depletion syndrome 13

Mitochondrial dna depletion syndrome 13 (encephalomyopathic type); mtdps13

Mitochondrial dna depletion syndrome 13, encephalomyopathic type

Mitochondrial dna depletion syndrome caused by mutation in fbxl4

Mitochondrial dna depletion syndrome type 13

Mtdna depletion syndrome

Mtdna depletion syndrome, encephalomyopathic form with variable craniofacial anomalies

Associated Genes (1)
 

NCBI-RefSeq:  FBXL4   (F-box and leucine rich repeat protein 4)

External Links:  gnomAD browser   Ensembl   GeneCards

 


Cross-references of Mitochondrial DNA depletion syndrome 13 OMIM GARD Orphanet NCBI-GTR NCBI-MedGen MalaCards      MeSH Annotations