Disease Aliases (19) | Dtna left ventricular noncompaction Left ventricular noncompaction 1 with or without congenital heart defects Lv non-compaction syndrome Lvnc Lvnc1 Left ventricular non-compaction syndrome Left ventricular noncompaction, isolated, autosomal dominant Left ventricular hypertrabeculation Left ventricular non-compaction cardiomyopathy Left ventricular noncompaction (disorder) Left ventricular noncompaction cardiomyopathy Noncompaction of left ventricular myocardium, familial isolated, autosomal dominant 1 Spongy myocardium Left ventricular noncompaction (disease) Left ventricular noncompaction 1 Left ventricular noncompaction 1; lvnc1 Left ventricular noncompaction caused by mutation in dtna Left ventricular noncompaction type 1 |
Associated Genes (14) NCBI-RefSeq: MYH7B (Myosin heavy chain 7B) External Links: gnomAD browser Ensembl GeneCards
NCBI-RefSeq: LDB3 (LIM domain binding 3) External Links: gnomAD browser Ensembl GeneCards
NCBI-RefSeq: ACTC1 (Actin alpha cardiac muscle 1) External Links: gnomAD browser Ensembl GeneCards
NCBI-RefSeq: PRDM16 (PR/SET domain 16) External Links: gnomAD browser Ensembl GeneCards
NCBI-RefSeq: TPM1 (Tropomyosin 1) External Links: gnomAD browser Ensembl GeneCards
NCBI-RefSeq: TNNT2 (Troponin T2, cardiac type) External Links: gnomAD browser Ensembl GeneCards
NCBI-RefSeq: MIB1 (MIB E3 ubiquitin protein ligase 1) External Links: gnomAD browser Ensembl GeneCards
NCBI-RefSeq: PLEKHM2 (Pleckstrin homology and RUN domain containing M2) External Links: gnomAD browser Ensembl GeneCards
NCBI-RefSeq: LMNA (Lamin A/C) External Links: gnomAD browser Ensembl GeneCards
NCBI-RefSeq: MIB2 (MIB E3 ubiquitin protein ligase 2) External Links: gnomAD browser Ensembl GeneCards
NCBI-RefSeq: DTNA (Dystrobrevin alpha) External Links: gnomAD browser Ensembl GeneCards
NCBI-RefSeq: PKP2 (Plakophilin 2) External Links: gnomAD browser Ensembl GeneCards
NCBI-RefSeq: MYBPC3 (Myosin binding protein C3) External Links: gnomAD browser Ensembl GeneCards
NCBI-RefSeq: MYH7 (Myosin heavy chain 7) External Links: gnomAD browser Ensembl GeneCards
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Cross-references of Left ventricular noncompaction cardiomyopathy | OMIM | GARD | Orphanet | NCBI-GTR | NCBI-MedGen | MalaCards | MeSH | Annotations |