GenTIGSA Gene Database on Rare Genetic Disorders
Laron-type Isolated Somatotropin Defect  
Disease Aliases (25)

Complete growth hormone insensitivity

Dwarfism ii, pituitary

Dwarfism iis, pituitary

Dwarfism, laron

Gh resistance, primary

Gh receptor deficiency

Growth hormone insensitivity syndrome

Growth hormone receptor deficiency

Growth hormone receptor defect

Laron dwarfism

Laron type dwarfism i

Laron syndrome

Laron type pituitary dwarfism i

Laron-type dwarfism

Laron-type isolated somatotropin defect

Pituitary dwarfism ii

Pituitary dwarfism iis

Primary gh resistance

Primary gh insensitivity

Primary growth hormone resistance

Primary growth hormone insensitivity

Severe gh insensitivity

Short stature due to growth hormone resistance

Syndrome, laron

Pituitary dwarfism 2

Associated Genes (1)
 

NCBI-RefSeq:  GHR   (Growth hormone receptor)

External Links:  gnomAD browser   Ensembl   GeneCards

 


Cross-references of Laron-type isolated somatotropin defect OMIM GARD Orphanet NCBI-GTR NCBI-MedGen MalaCards      MeSH Annotations