GenTIGSA Gene Database on Rare Genetic Disorders
Isovaleryl-CoA Dehydrogenase Deficiency  
Disease Aliases (12)

Acidemia, isovaleric

Isovaleric acid coa dehydrogenase deficiency

Iva

Ivd deficiency

Isovaleric acid-coa dehydrogenase deficiency

Isovaleric acidemia

Isovalericacidemia

Isovaleryl coa carboxylase deficiency

Isovaleryl-coa dehydrogenase deficiency

Isovaleryl-coenzyme a dehydrogenase deficiency

Isovaleric acidemia; iva

Isovaleric aciduria

Associated Genes (1)
 

NCBI-RefSeq:  IVD   (Isovaleryl-CoA dehydrogenase)

External Links:  gnomAD browser   Ensembl   GeneCards

 


Cross-references of Isovaleryl-CoA dehydrogenase deficiency OMIM GARD Orphanet NCBI-GTR NCBI-MedGen MalaCards      MeSH Annotations