GenTIGSA Gene Database on Rare Genetic Disorders
Hyperinsulinemic Hypoglycemia, Familial, 4  
Disease Aliases (32)

3-@hydroxyacyl-coa dehydrogenase deficiency

3-alpha-hydroxyacyl-coenzyme a dehydrogenase deficiency

3-hydroxyacyl-coenzyme a dehydrogenase deficiency

3-alpha hydroxyacyl-coa dehydrogenase deficiency

3-hydroxyacyl-coa dehydrogenase deficiency

3-hydroxylacyl-coa dehydrogenase deficiency

Deficiency of 3-hydroxyacyl-coa dehydrogenase

Deficiency of beta-hydroxyacyl dehydrogenase

Deficiency of beta-keto-reductase

Had deficiency

Hadh deficiency

Hadh hyperinsulinemic hypoglycemia (disease)

Hadh-related hyperinsulinism

Hadhsc deficiency

Hhf4

Hyperinsulinemic hypoglycemia due to short chain 3-hydroxylacyl-coa dehydrogenase deficiency

Hyperinsulinism due to hadh deficiency

Hyperinsulinism due to schad deficiency

Hyperinsulinism due to glutamodehydrogenase deficiency

Hyperinsulinism due to short chain 3-hydroxyacyl-coenzyme a dehydrogenase deficiency

L-3-alpha-hydroxyacyl-coa dehydrogenase, short chain, deficiency

M-schad deficiency

M/schad

Medium and short chain 3-hydroxyacyl-coa dehydrogenase deficiency

Schad deficiency, formerly

Schad deficiency

Hyperinsulinemic hypoglycemia (disease) caused by mutation in hadh

Hyperinsulinemic hypoglycemia due to hadh deficiency

Hyperinsulinemic hypoglycemia, familial, 4

Hyperinsulinemic hypoglycemia, familial, 4; hhf4

Hyperinsulinemic hypoglycemia, familial, type 4

Hyperinsulinism due to short chain 3-hydroxylacyl-coa dehydrogenase deficiency

Associated Genes (1)
 

NCBI-RefSeq:  HADH   (Hydroxyacyl-CoA dehydrogenase)

External Links:  gnomAD browser   Ensembl   GeneCards

 


Cross-references of Hyperinsulinemic hypoglycemia, familial, 4 OMIM GARD Orphanet NCBI-GTR NCBI-MedGen MalaCards      MeSH Annotations