GenTIGSA Gene Database on Rare Genetic Disorders
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GTP Cyclohydrolase I Deficiency With Hyperphenylalaninemia  
Disease Aliases (19)

Dystonia, dopa-responsive, with or without hyperphenylalaninemia, autosomal recessive

Gtp - guanosine-5-triphosphate cyclohydrolase deficiency

Gtp cyclohydrolase 1 deficiency (gtpch)

Gtp cyclohydrolase 1-related disorders

Gtp cyclohydrolase 1 deficiency

Gtp-cyclohydrolase i deficiency

Gtpch deficiency

Guanosine triphosphate (gtp) cyclohydrolase i deficiency

Guanosine triphosphate cyclohydrolase i deficiency

Guanosine-5-triphosphate cyclohydrolase deficiency

Hpabh4b

Hyperphenylalaninemia, tetrahydrobiopterin-deficient, due to gtp cyclohydrolase i deficiency

Hyperphenylalaninemia due to gtp cyclohydrolase deficiency

Hyperphenylalaninemia with neopterin deficiency

Hyperphenylalaninemia, bh4-deficient, b

Hyperphenylalaninemia, tetrahydrobiopterin-deficient, due to gtp cyclohydrolase 1 deficiency

Hyperphenylalaninemia, bh4-deficient, b; hpabh4b

Hyperphenylalaninemia, bh4-deficient, type b

Associated Genes (1)
 

NCBI-RefSeq:  GCH1   (GTP cyclohydrolase 1)

External Links:  gnomAD browser   Ensembl   GeneCards

 


Cross-references of GTP cyclohydrolase I deficiency with hyperphenylalaninemia OMIM GARD Orphanet NCBI-GTR NCBI-MedGen MalaCards      MeSH Annotations