GenTIGSA Gene Database on Rare Genetic Disorders
  Beta Version
Epidermolytic Ichthyosis  
Disease Aliases (38)

Autosomal dominant epidermolytic ichthyosis

Bcie

Bie

Bie - bullous ichthyosiform erythroderma

Bullous congenital ichthyosiform erythroderma

Bullous erythroderma ichthyosiformis congenita of brocq

Bullous ichthyosiform erythroderma

Bullous erythroderma ichthyosiforme

Bullous erythroderma ichthyosiformes

Bullous ichthyosiform erythroderma congenital

Bullous ichthyosiform erythrodermas

Bullous congenital ichthyosiform erythroderma of brock

Bullous ichthyosiform erythroderma congenita

Bullous ichthyosis

Congenital bullous ichthyosiform erythroderma

Congenital ichthyosiform erythroderma, bullous

Dominant ichthyosis vulgaris

Ehk

Ei

Epidermolytic hyperkeratosis, late-onset

Epidermolytic ichthyosis

Epidermolytic hyperkeratoses

Epidermolytic hyperkeratosis

Epidermolytic palmoplantar hyperkeratosis

Erythroderma ichthyosiforme, bullous

Erythroderma ichthyosiformes, bullous

Erythroderma, bullous ichthyosiform

Erythrodermas, bullous ichthyosiform

Hyperkeratoses, epidermolytic

Hyperkeratosis, epidermolytic

Ichthyosiform erythroderma, bullous

Ichthyosiform erythroderma, bullous congenital

Ichthyosiform erythrodermas, bullous

Ichthyosiforme, bullous erythroderma

Ichthyosiformes, bullous erythroderma

Ichthyosis hystrix brocq type

Krt1-related epidermolytic hyperkeratosis

Epidermolytic hyperkeratosis; ehk

Associated Genes (2)
 

NCBI-RefSeq:  KRT1   (Keratin 1)

External Links:  gnomAD browser   Ensembl   GeneCards

 

NCBI-RefSeq:  KRT10   (Keratin 10)

External Links:  gnomAD browser   Ensembl   GeneCards

 


Cross-references of Epidermolytic ichthyosis OMIM GARD Orphanet NCBI-GTR NCBI-MedGen MalaCards      MeSH Annotations