GenTIGSA Gene Database on Rare Genetic Disorders
Desbuquois Dysplasia 1  
Disease Aliases (13)

Cant1 desbuquois dysplasia

Dbqd

Dbqd1

Desbuquois dysplasia 1, kim variant

Desbuquois dysplasia, kim variant

Desbuquois syndrome

Desbuquois dysplasia 1

Desbuquois dysplasia 1; dbqd1

Desbuquois dysplasia caused by mutation in cant1

Desbuquois dysplasia type 1

Micromelic dwarfism with vertebral and metaphyseal abnormalities and advanced carpotarsal ossification

Micromelic dwarfism, narrow chest, vertebral and metaphyseal abnormalities and advanced carpotarsal ossification

Associated Genes (2)
 

NCBI-RefSeq:  CANT1   (Calcium activated nucleotidase 1)

External Links:  gnomAD browser   Ensembl   GeneCards

 

NCBI-RefSeq:  XYLT1   (Xylosyltransferase 1)

External Links:  gnomAD browser   Ensembl   GeneCards

 


Cross-references of Desbuquois dysplasia 1 OMIM GARD Orphanet NCBI-GTR NCBI-MedGen MalaCards      MeSH Annotations