GenTIGSA Gene Database on Rare Genetic Disorders
Congenital Adrenal Hypoplasia, X-linked  
Disease Aliases (32)

Addison disease, x-linked

Adrenal hypoplasia, congenital, with hypogonadotropic hypogonadism

Ahc

Ahc with hhg

Ahc with isolated gonadotropin deficiency

Ahch

Ahx

Addison disease, x linked

Adrenal hypoplasia congenita

Cytomegalic adrenocortical hypoplasia

Congenital adrenal hypoplasias

Congenital adrenal hypoplasia, x-linked

Cytomegalic adrenocortical hypoplasias

Familial x linked addison disease

Familial x-linked addison disease

Hypoplasia, congenital adrenal

Isolated x-linked adrenal hypoplasia congenita

X linked adrenal hypoplasia

X linked congenital adrenal hypoplasia

X-linked addison disease

X-linked adrenal hypoplasia congenita

X-linked ahc

X-linked adrenal hypoplasia

X-linked congenital adrenal hypoplasia

Adrenal hypoplasia, congenital

Adrenal hypoplasia, congenital, with precocious puberty

Adrenal hypoplasia, congenital; ahc

Adrenal insufficiency, progressive, and hypogonadotropic hypogonadism

Cytomegalic congenital adrenal hypoplasia

Mineralocorticoid deficiency, isolated

Associated Genes (1)
 

NCBI-RefSeq:  NR0B1   (Nuclear receptor subfamily 0 group B member 1)

External Links:  gnomAD browser   Ensembl   GeneCards

 


Cross-references of Congenital adrenal hypoplasia, X-linked OMIM GARD Orphanet NCBI-GTR NCBI-MedGen MalaCards      MeSH Annotations