GenTIGSA Gene Database on Rare Genetic Disorders
Biotin-responsive Basal Ganglia Disease  
Disease Aliases (14)

Basal ganglia disease, biotin-responsive

Bbgd

Btbgd

Biotin-responsive basal ganglia disease

Biotin-thiamine-responsive basal ganglia disease

Encephalopathy, thiamine-responsive

Thiamine metabolism dysfunction syndrome 2 (biotin- or thiamine-responsive type)

Thmd2

Thiamine metabolism dysfunction syndrome 2

Thiamine metabolism dysfunction syndrome 2 (biotin- or thiamine-responsive encephalopathy type 2)

Thiamine metabolism dysfunction syndrome type 2

Thiamine transporter-2 deficiency

Thiamine-responsive encephalopathy

Thiamine metabolism dysfunction syndrome 2 (biotin- or thiamine-responsive type); thmd2

Associated Genes (1)
 

NCBI-RefSeq:  SLC19A3   (Solute carrier family 19 member 3)

External Links:  gnomAD browser   Ensembl   GeneCards

 


Cross-references of Biotin-responsive basal ganglia disease OMIM GARD Orphanet NCBI-GTR NCBI-MedGen MalaCards      MeSH Annotations