GenTIGSA Gene Database on Rare Genetic Disorders
Arrhythmogenic Cardiomyopathy With Wooly Hair And Keratoderma  
Disease Aliases (20)

Carvajal syndrome

Cardiomyopathy dilated with woolly hair and keratoderma

Cardiomyopathy, dilated, with woolly hair and keratoderma

Dcwhk

Epidermolytic palmoplantar keratoderma woolly hair and dilated cardiomyopathy

Epidermolytic palmoplantar keratoderma, woolly hair, and dilated cardiomyopathy

Kwwh type ii

Keratoderma with woolly hair type ii

Keratoderma with wooly hair type ii

Palmoplantar keratoderma with left ventricular cardiomyopathy and woolly hair

Woolly hair-palmoplantar hyperkeratosis-dilated cardiomyopathy syndrome

Woolly hair-palmoplantar keratoderma-dilated cardiomyopathy syndrome

Wooly hair - palmoplantar keratoderma - dilated cardiomyopathy

Wooly hair and palmoplantar keratoderma with dilated cardiomyopathy syndrome

Wooly hair-palmoplantar hyperkeratosis-dilated cardiomyopathy syndrome

Wooly hair-palmoplantar keratoderma-dilated cardiomyopathy syndrome

Arrhythmogenic cardiomyopathy with woolly hair and keratoderma

Cardiomyopathy, dilated, with woolly hair and keratoderma; dcwhk

Dilated cardiomyopathy with woolly hair and keratoderma

Woolly hair - palmoplantar keratoderma - dilated cardiomyopathy syndrome

Associated Genes (1)
 

NCBI-RefSeq:  DSP   (Desmoplakin)

External Links:  gnomAD browser   Ensembl   GeneCards

 


Cross-references of Arrhythmogenic cardiomyopathy with wooly hair and keratoderma OMIM GARD Orphanet NCBI-GTR NCBI-MedGen MalaCards      MeSH Annotations