GenTIGSA Gene Database on Rare Genetic Disorders
Antley-Bixler Syndrome With Genital Anomalies And Disordered Steroidogenesis  
Disease Aliases (8)

Adrenal hyperplasia, congenital, due to cytochrome p450 oxidoreductase deficiency

Congenital adrenal hyperplasia due to cytochrome p450 oxidoreductase deficiency

Congenital adrenal hyperplasia due to cytochrome por deficiency

Disordered steroidogenesis due to por deficiency

Disordered steroidogenesis due to cytochrome p450 oxidoreductase

Por deficiency

Pord

Disordered steroidogenesis due to cytochrome p450 oxidoreductase deficiency

Associated Genes (1)
 

NCBI-RefSeq:  POR   (Cytochrome p450 oxidoreductase)

External Links:  gnomAD browser   Ensembl   GeneCards

 


Cross-references of Antley-Bixler syndrome with genital anomalies and disordered steroidogenesis OMIM GARD Orphanet NCBI-GTR NCBI-MedGen MalaCards      MeSH Annotations