GenTIGSA Gene Database on Rare Genetic Disorders
3-Oxo-5 Alpha-steroid Delta 4-dehydrogenase Deficiency  
Disease Aliases (11)

46,xy disorder of sex development due to 5-alpha-reductase 2 deficiency

46,xy dsd due to 5-alpha-reductase 2 deficiency

5 alpha steroid reductase 2 deficiency

Familial incomplete male pseudohermaphroditism type 2

Familial incomplete male pseudohermaphroditism, type 2

Male pseudohermaphroditism due to 5-alpha-reductase 2 deficiency

Male pseudohermaphroditism due to 5-alpha-reductase deficiency

Ppsh

Ppsh - pseudovaginal perineoscrotal hypospadias

Pseudovaginal perineoscrotal hypospadias

Steroid 5-alpha-reductase 2 deficiency

Associated Genes (0)
 

Cross-references of 3-Oxo-5 alpha-steroid delta 4-dehydrogenase deficiency OMIM GARD Orphanet NCBI-GTR NCBI-MedGen MalaCards      MeSH Annotations