GenTIGSA Gene Database on Rare Genetic Disorders
  Beta Version

Variants from 496 rare genetic disorders, with a total of 857 reported, submitted from India

von Willebrand disease

An  Autosomal dominant, Autosomal recessive  mode(s) within the Blood disorders  category

Likely pathogenic 1
Pathogenic/Likely pathogenic 1
Uncertain significance 1

Variant name Variant type Phenotype Germline classification Molecular consequence dbSNP_ID Submitter
NM_000552.5(VWF):c.3944G>A (p.Arg1315His) Single nucleotide variant von Willebrand disease type 2M Likely pathogenic missense variant rs61749396
NM_000552.5(VWF):c.3943C>T (p.Arg1315Cys) Single nucleotide variant not provided

 

von Willebrand disorder

 

Hereditary von Willebrand disease

 

von Willebrand disease type 1

 

VWF-related disorder
Pathogenic/Likely pathogenic missense variant rs61749395
NM_000552.5(VWF):c.3835G>A (p.Val1279Ile) Single nucleotide variant von Willebrand disease type 1

 

not specified

 

not provided

 

Hereditary von Willebrand disease

 

von Willebrand disease type 2

 

Thrombocytopenia
Uncertain significance missense variant rs61749376

Graph displaying all Indian institutes, the rare genetic disorders they studied, and the variants submitted to ClinVar