GenTIGSA Gene Database on Rare Genetic Disorders

Variants in ClinVar from 582 of 1004 Rare Genetic Disorders of GenTIGS

von Willebrand disease

An  Autosomal dominant, Autosomal recessive  mode(s) within the Blood disorders  category

Likely pathogenic 1
Pathogenic/Likely pathogenic 1
Uncertain significance 1

Variant name Variant type GRCH38 location Germline classification Molecular consequence dbSNP_ID Submitter
NM_000552.5(VWF):c.3944G>A (p.Arg1315His) Single nucleotide variant Chr12:6019474 Likely pathogenic Missense variant rs61749396
NM_000552.5(VWF):c.3943C>T (p.Arg1315Cys) Single nucleotide variant Chr12:6019475 Pathogenic/Likely pathogenic Missense variant rs61749395
NM_000552.5(VWF):c.3835G>A (p.Val1279Ile) Single nucleotide variant Chr12:6019583 Uncertain significance Missense variant rs61749376

Indian Institutes & Variant Submission Overview
Chromosome-wise Variant Distribution