GenTIGSA Gene Database on Rare Genetic Disorders

Variants in ClinVar from 539 of 916 Rare Genetic Disorders of GenTIGS

Thrombophilia due to thrombin defect

An  Autosomal dominant  mode(s) within the Blood disorders  category

Pathogenic/Likely pathogenic 3
Pathogenic/Likely pathogenic/Pathogenic, low penetrance; risk factor 1

Variant name Variant type GRCH38 location Germline classification Molecular consequence dbSNP_ID Submitter
NM_000506.5(F2):c.*97G>A Single nucleotide variant Chr11:46739505 Pathogenic/Likely pathogenic/Pathogenic, low penetrance; risk factor rs1799963
NM_005957.5(MTHFR):c.459C>G (p.Ile153Met) Single nucleotide variant Chr1:11801177 Pathogenic/Likely pathogenic Missense variant rs767890671 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
.Neuberg Centre For Genomic Medicine, NCGM
NM_005957.5(MTHFR):c.548G>A (p.Arg183Gln) Single nucleotide variant Chr1:11800250 Pathogenic/Likely pathogenic Missense variant rs574132670 .Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics
.Neuberg Centre For Genomic Medicine, NCGM
NM_005957.5(MTHFR):c.202C>G (p.Arg68Gly) Single nucleotide variant Chr1:11802915 Pathogenic/Likely pathogenic Missense variant rs763539350 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
.Neuberg Centre For Genomic Medicine, NCGM

Indian Institutes & Variant Submission Overview
Chromosome-wise Variant Distribution