GenTIGSA Gene Database on Rare Genetic Disorders

Variants in ClinVar from 539 of 916 Rare Genetic Disorders of GenTIGS

Tetralogy of Fallot

An  Autosomal dominant  mode(s) within the Cardiovascular disorders  category

Likely pathogenic 1
Pathogenic/Likely pathogenic 1
Uncertain significance 1

Variant name Variant type GRCH38 location Germline classification Molecular consequence dbSNP_ID Submitter
NM_001308093.3(GATA4):c.25G>A (p.Ala9Thr) Single nucleotide variant Chr8:11708337 Uncertain significance Missense variant|intron variant rs864321699 .Cytogenetics- Mohapatra Lab, Banaras Hindu University
NM_004387.4(NKX2-5):c.443C>A (p.Ala148Glu) Single nucleotide variant Chr5:173233101 Likely pathogenic 3 prime UTR variant|missense variant rs864321649 .Cytogenetics- Mohapatra Lab, Banaras Hindu University
NM_020975.6(RET):c.2753T>C (p.Met918Thr) Single nucleotide variant Chr10:43121968 Pathogenic/Likely pathogenic Missense variant rs74799832 .Laboratory of Molecular and Cytogenetics, Department of Anatomy, All India Institute of Medical Sciences (AIIMS)

Indian Institutes & Variant Submission Overview
Chromosome-wise Variant Distribution