GenTIGSA Gene Database on Rare Genetic Disorders
  Beta Version

Variants from 540 rare genetic disorders, with a total of 916 reported, submitted from India

Syndromic microphthalmia type 5

An  Autosomal dominant  mode(s) within the Eye disorders  category

Likely pathogenic 1

Variant name Variant type GRCH38 location Germline classification Molecular consequence dbSNP_ID Submitter
NM_021728.4(OTX2):c.278G>T (p.Trp93Leu) Single nucleotide variant Chr14:56802351 Likely pathogenic Missense variant|non-coding transcript variant rs2139529394 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India

Graph displaying all Indian institutes, the rare genetic disorders they studied, and the variants submitted to ClinVar (Indian ClinVar data)

Chromosome-wise variant distribution in rare genetic disorders (Indian ClinVar data).