GenTIGSA Gene Database on Rare Genetic Disorders
  Beta Version

Variants from 496 rare genetic disorders, with a total of 857 reported, submitted from India

Spastic ataxia

An  Autosomal dominant, Autosomal recessive  mode(s) within the Neurodegenerative disorders  category

Likely pathogenic 2
Pathogenic 2
Pathogenic/Likely pathogenic 1

Variant name Variant type Germline classification Molecular consequence Grch38 Location dbSNP_ID Submitter
NM_006796.3(AFG3L2):c.1951A>G (p.Arg651Gly) single nucleotide variant Likely pathogenic missense variant Chr18:12340230 rs764254189 .Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics
NM_177400.3(NKX6-2):c.516C>G (p.Tyr172Ter) single nucleotide variant Pathogenic nonsense Chr10:132785343 rs2134706418 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_014363.6(SACS):c.2185+1G>T single nucleotide variant Likely pathogenic splice donor variant Chr13:23353784 rs2542384410 .Lifecell International Pvt. Ltd
NM_014363.6(SACS):c.9305T>A (p.Leu3102Ter) single nucleotide variant Pathogenic nonsense Chr13:23334571 rs886041949 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_003119.4(SPG7):c.2228T>C (p.Ile743Thr) single nucleotide variant Pathogenic/Likely pathogenic 3 prime UTR variant|missense variant Chr16:89556933 rs752623413 .Lifecell International Pvt. Ltd
.Neuberg Centre For Genomic Medicine, NCGM

Graph displaying all Indian institutes, the rare genetic disorders they studied, and the variants submitted to ClinVar