GenTIGSA Gene Database on Rare Genetic Disorders
  Beta Version

Variants from 536 rare genetic disorders, with a total of 897 reported, submitted from India

Severe early-childhood-onset retinal dystrophy

An  Autosomal recessive  mode(s) within the Eye disorders  category

Pathogenic 1
Pathogenic/Likely pathogenic 1
Uncertain significance 1

Variant name Variant type GRCH38 location Germline classification Molecular consequence dbSNP_ID Submitter
NM_000350.3(ABCA4):c.1645G>A (p.Ala549Thr) Single nucleotide variant Chr1:94063227 Uncertain significance Missense variant rs61748557 .Strand Center for Genomics and Personalized Medicine, Strand Life Sciences Pvt Ltd
NM_000350.3(ABCA4):c.4838del (p.Asp1613fs) Deletion Chr1:94021650 Pathogenic/Likely pathogenic Frameshift variant rs61752438 .Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics
NM_019098.5(CNGB3):c.1781+1G>T Single nucleotide variant Chr8:86604092 Pathogenic Splice donor variant rs1375507464 .Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics

Graph displaying all Indian institutes, the rare genetic disorders they studied, and the variants submitted to ClinVar