GenTIGSA Gene Database on Rare Genetic Disorders
  Beta Version

Variants from 536 rare genetic disorders, with a total of 897 reported, submitted from India

Renal tubular acidosis with progressive nerve deafness

An  Autosomal recessive  mode(s) within the Multisystemic disorders  category

Conflicting classifications of pathogenicity 1
Likely pathogenic 2
Pathogenic 1
Pathogenic/Likely pathogenic 1

Variant name Variant type GRCH38 location Germline classification Molecular consequence dbSNP_ID Submitter
NM_001692.4(ATP6V1B1):c.1060G>A (p.Asp354Asn) Single nucleotide variant Chr2:70963312 Likely pathogenic Missense variant rs782484337 .Laboratory of Cyto-molecular Genetics, Department of Anatomy, All India Institute of Medical Sciences (AIIMS), New Delhi
NM_001692.4(ATP6V1B1):c.1449G>T (p.Lys483Asn) Single nucleotide variant Chr2:70965028 Likely pathogenic Missense variant rs2104834809 .Laboratory of Cyto-molecular Genetics, Department of Anatomy, All India Institute of Medical Sciences (AIIMS), New Delhi
NM_001692.4(ATP6V1B1):c.925G>T (p.Glu309Ter) Single nucleotide variant Chr2:70963177 Pathogenic Nonsense rs2104831698 .Kamineni Academy of Medical Sciences & Research Centre, Kamineni Hospitals
NM_001692.4(ATP6V1B1):c.67C>T (p.Arg23Ter) Single nucleotide variant Chr2:70936021 Pathogenic/Likely pathogenic Nonsense rs1553415274 .Laboratory of Cyto-molecular Genetics, Department of Anatomy, All India Institute of Medical Sciences (AIIMS), New Delhi
NM_001692.4(ATP6V1B1):c.481G>A (p.Glu161Lys) Single nucleotide variant Chr2:70959974 Conflicting classifications of pathogenicity Missense variant rs114234874 .Laboratory of Cyto-molecular Genetics, Department of Anatomy, All India Institute of Medical Sciences (AIIMS), New Delhi

Graph displaying all Indian institutes, the rare genetic disorders they studied, and the variants submitted to ClinVar